E70.0
Billable

Classical phenylketonuria

Billable / Specific Code

What is Classical phenylketonuria?

ICD-10-CM E70.0 is the diagnosis code for Classical phenylketonuria. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

Coding Guidelines for E70.0

Always refer to the official ICD-10-CM Tabular List for complete coding guidelines. Ensure documentation supports the specificity of the code selected. When in doubt, consult a certified medical coder or the latest CMS guidelines.

ICD-10-CM Code Hierarchy

Understanding where E70.0 sits in the ICD-10-CM classification helps ensure proper coding:

Related Codes

Frequently Asked Questions

Is E70.0 a billable ICD-10-CM code?

Yes, E70.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What does E70.0 mean?

E70.0 is the ICD-10-CM diagnosis code for "Classical phenylketonuria". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of E70.0?

The parent code of E70.0 is E70 ("Disorders of aromatic amino-acid metabolism"). E70.0 provides a more specific classification within this category.

What section is E70.0 in?

E70.0 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.

When should I use E70.0?

Use E70.0 when the patients documented diagnosis matches "Classical phenylketonuria" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Classical phenylketonuria?

The ICD-10-CM code for Classical phenylketonuria is E70.0.

Can E70.0 be used for primary diagnosis?

Yes, E70.0 can be used as a primary diagnosis code since it is billable and specific.

What chapter is E70.0 in?

E70.0 is in Chapter 4 of the ICD-10-CM Tabular List.

Is E70.0 valid for 2026?

Yes, E70.0 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousE70Disorders of aromatic amino-acid metabolismNext →E70.1Other hyperphenylalaninemias
Code Details
E70.0
Classical phenylketonuria
Billable / Specific Code
4 — Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 — Metabolic disorders
2026 ICD-10-CM