ICD-10-CM E71.110 is the diagnosis code for Isovaleric acidemia. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.
Always refer to the official ICD-10-CM Tabular List for complete coding guidelines. Ensure documentation supports the specificity of the code selected. When in doubt, consult a certified medical coder or the latest CMS guidelines.
Understanding where E71.110 sits in the ICD-10-CM classification helps ensure proper coding:
Yes, E71.110 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
E71.110 is the ICD-10-CM diagnosis code for "Isovaleric acidemia". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.
The parent code of E71.110 is E71.11 ("Branched-chain organic acidurias"). E71.110 provides a more specific classification within this category.
E71.110 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.
Use E71.110 when the patients documented diagnosis matches "Isovaleric acidemia" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.
The ICD-10-CM code for Isovaleric acidemia is E71.110.
Yes, E71.110 can be used as a primary diagnosis code since it is billable and specific.
E71.110 is in Chapter 4 of the ICD-10-CM Tabular List.
Yes, E71.110 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.