ICD-10-CM E71.111 is the diagnosis code for 3-methylglutaconic aciduria. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.
Always refer to the official ICD-10-CM Tabular List for complete coding guidelines. Ensure documentation supports the specificity of the code selected. When in doubt, consult a certified medical coder or the latest CMS guidelines.
Understanding where E71.111 sits in the ICD-10-CM classification helps ensure proper coding:
Yes, E71.111 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
E71.111 is the ICD-10-CM diagnosis code for "3-methylglutaconic aciduria". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.
The parent code of E71.111 is E71.11 ("Branched-chain organic acidurias"). E71.111 provides a more specific classification within this category.
E71.111 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.
Use E71.111 when the patients documented diagnosis matches "3-methylglutaconic aciduria" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.
The ICD-10-CM code for 3-methylglutaconic aciduria is E71.111.
Yes, E71.111 can be used as a primary diagnosis code since it is billable and specific.
E71.111 is in Chapter 4 of the ICD-10-CM Tabular List.
Yes, E71.111 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.