E71.3
Non-Billable

Disorders of fatty-acid metabolism

Non-Billable / Non-Specific Code

What is Disorders of fatty-acid metabolism?

ICD-10-CM E71.3 is the diagnosis code for Disorders of fatty-acid metabolism. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a non-billable/non-specific ICD-10-CM code that should not be used for reimbursement. A more specific sub-code is required for billing. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

⛔ Excludes1
â„šī¸ Excludes2

Coding Guidelines for E71.3

⛔ Type 1 Excludes (Never code together)

The following conditions should never be coded at the same time as E71.3. They are mutually exclusive:

  • peroxisomal disorders (E71.5)
  • Refsum's disease (G60.1)
  • Schilder's disease (G37.0)

â„šī¸ Type 2 Excludes (Code separately if applicable)

The following conditions are not included in E71.3. If the patient has both, code each condition separately:

  • carnitine deficiency due to inborn error of metabolism (E71.42)

ICD-10-CM Code Hierarchy

Understanding where E71.3 sits in the ICD-10-CM classification helps ensure proper coding:

Sub-Codes 4 entries
E71.30Disorder of fatty-acid metabolism, unspecifiedBillableE71.31Disorders of fatty-acid oxidationNon-BillableE71.310Long chain/very long chain acyl CoA dehydrogenase deficiencyBillableE71.311Medium chain acyl CoA dehydrogenase deficiencyBillableE71.312Short chain acyl CoA dehydrogenase deficiencyBillableE71.313Glutaric aciduria type IIBillableE71.314Muscle carnitine palmitoyltransferase deficiencyBillableE71.318Other disorders of fatty-acid oxidationBillableE71.32Disorders of ketone metabolismBillableE71.39Other disorders of fatty-acid metabolismBillable
Related Codes

Frequently Asked Questions

Is E71.3 a billable ICD-10-CM code?

No, E71.3 is a non-billable/non-specific code. You should use a more specific sub-code for billing and reimbursement.

What does E71.3 mean?

E71.3 is the ICD-10-CM diagnosis code for "Disorders of fatty-acid metabolism". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of E71.3?

The parent code of E71.3 is E71 ("Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism"). E71.3 provides a more specific classification within this category.

What section is E71.3 in?

E71.3 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.

What are the sub-codes of E71.3?

E71.3 has 4 sub-code(s) that provide more specific detail: E71.30, E71.31, E71.32, E71.39.

When should I use E71.3?

Use E71.3 when the patients documented diagnosis matches "Disorders of fatty-acid metabolism" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Disorders of fatty-acid metabolism?

The ICD-10-CM code for Disorders of fatty-acid metabolism is E71.3.

Can E71.3 be used for primary diagnosis?

No, E71.3 is non-billable. Use a more specific sub-code for primary diagnosis billing.

What chapter is E71.3 in?

E71.3 is in Chapter 4 of the ICD-10-CM Tabular List.

What conditions are excluded from E71.3?

Type 1 Excludes for E71.3 include: peroxisomal disorders (E71.5); Refsum's disease (G60.1); Schilder's disease (G37.0).

Is E71.3 valid for 2026?

Yes, E71.3 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousE71.2Disorder of branched-chain amino-acid metabolism, unspecifiedNext →E71.30Disorder of fatty-acid metabolism, unspecified
Code Details
E71.3
Disorders of fatty-acid metabolism
Non-Billable / Non-Specific Code
4 — Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 — Metabolic disorders
2026 ICD-10-CM