E71.51
Non-Billable

Disorders of peroxisome biogenesis

Non-Billable / Non-Specific Code

What is Disorders of peroxisome biogenesis?

ICD-10-CM E71.51 is the diagnosis code for Disorders of peroxisome biogenesis. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a non-billable/non-specific ICD-10-CM code that should not be used for reimbursement. A more specific sub-code is required for billing. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

💡 Inclusions
⛔ Excludes1

Coding Guidelines for E71.51

✅ This Code Includes

  • Group 1 peroxisomal disorders

⛔ Type 1 Excludes (Never code together)

The following conditions should never be coded at the same time as E71.51. They are mutually exclusive:

  • Refsum's disease (G60.1)

ICD-10-CM Code Hierarchy

Understanding where E71.51 sits in the ICD-10-CM classification helps ensure proper coding:

Current CodeE71.51 — Disorders of peroxisome biogenesis
Sub-Codes 3 entries
E71.510Zellweger syndromeBillableE71.511Neonatal adrenoleukodystrophyBillableE71.518Other disorders of peroxisome biogenesisBillable
Related Codes

Frequently Asked Questions

Is E71.51 a billable ICD-10-CM code?

No, E71.51 is a non-billable/non-specific code. You should use a more specific sub-code for billing and reimbursement.

What does E71.51 mean?

E71.51 is the ICD-10-CM diagnosis code for "Disorders of peroxisome biogenesis". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of E71.51?

The parent code of E71.51 is E71.5 ("Peroxisomal disorders"). E71.51 provides a more specific classification within this category.

What section is E71.51 in?

E71.51 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.

What are the sub-codes of E71.51?

E71.51 has 3 sub-code(s) that provide more specific detail: E71.510, E71.511, E71.518.

When should I use E71.51?

Use E71.51 when the patients documented diagnosis matches "Disorders of peroxisome biogenesis" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Disorders of peroxisome biogenesis?

The ICD-10-CM code for Disorders of peroxisome biogenesis is E71.51.

Can E71.51 be used for primary diagnosis?

No, E71.51 is non-billable. Use a more specific sub-code for primary diagnosis billing.

What chapter is E71.51 in?

E71.51 is in Chapter 4 of the ICD-10-CM Tabular List.

What conditions are excluded from E71.51?

Type 1 Excludes for E71.51 include: Refsum's disease (G60.1).

Is E71.51 valid for 2026?

Yes, E71.51 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousE71.50Peroxisomal disorder, unspecifiedNext →E71.510Zellweger syndrome
Code Details
E71.51
Disorders of peroxisome biogenesis
Non-Billable / Non-Specific Code
4 — Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 — Metabolic disorders
2026 ICD-10-CM