E77.0
Billable

Defects in post-translational modification of lysosomal enzymes

Billable / Specific Code

What is Defects in post-translational modification of lysosomal enzymes?

ICD-10-CM E77.0 is the diagnosis code for Defects in post-translational modification of lysosomal enzymes. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

💡 Inclusions

Coding Guidelines for E77.0

✅ This Code Includes

  • Mucolipidosis II [I-cell disease]
  • Mucolipidosis III [pseudo-Hurler polydystrophy]

ICD-10-CM Code Hierarchy

Understanding where E77.0 sits in the ICD-10-CM classification helps ensure proper coding:

Current CodeE77.0 — Defects in post-translational modification of lysosomal enzymes
Related Codes

Frequently Asked Questions

Is E77.0 a billable ICD-10-CM code?

Yes, E77.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What does E77.0 mean?

E77.0 is the ICD-10-CM diagnosis code for "Defects in post-translational modification of lysosomal enzymes". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of E77.0?

The parent code of E77.0 is E77 ("Disorders of glycoprotein metabolism"). E77.0 provides a more specific classification within this category.

What section is E77.0 in?

E77.0 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.

When should I use E77.0?

Use E77.0 when the patients documented diagnosis matches "Defects in post-translational modification of lysosomal enzymes" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Defects in post-translational modification of lysosomal enzymes?

The ICD-10-CM code for Defects in post-translational modification of lysosomal enzymes is E77.0.

Can E77.0 be used for primary diagnosis?

Yes, E77.0 can be used as a primary diagnosis code since it is billable and specific.

What chapter is E77.0 in?

E77.0 is in Chapter 4 of the ICD-10-CM Tabular List.

Is E77.0 valid for 2026?

Yes, E77.0 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousE77Disorders of glycoprotein metabolismNext →E77.1Defects in glycoprotein degradation
Code Details
E77.0
Defects in post-translational modification of lysosomal enzymes
Billable / Specific Code
4 — Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 — Metabolic disorders
2026 ICD-10-CM