N01
Non-Billable

Rapidly progressive nephritic syndrome

Non-Billable / Non-Specific Code

What is Rapidly progressive nephritic syndrome?

ICD-10-CM N01 is the diagnosis code for Rapidly progressive nephritic syndrome. This code falls under the section "Glomerular diseases" within Chapter 14 — Diseases of the genitourinary system (N00-N99). It is a non-billable/non-specific ICD-10-CM code that should not be used for reimbursement. A more specific sub-code is required for billing. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

⛔ Excludes1

Coding Guidelines for N01

⛔ Type 1 Excludes (Never code together)

The following conditions should never be coded at the same time as N01. They are mutually exclusive:

  • nephritic syndrome NOS (N05.-)

ICD-10-CM Code Hierarchy

Understanding where N01 sits in the ICD-10-CM classification helps ensure proper coding:

Sub-Codes 11 entries
N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormalityBillableN01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesionsBillableN01.2Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritisBillableN01.3Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritisBillableN01.4Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritisBillableN01.5Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritisBillableN01.6Rapidly progressive nephritic syndrome with dense deposit diseaseBillableN01.7Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritisBillableN01.8Rapidly progressive nephritic syndrome with other morphologic changesBillableN01.9Rapidly progressive nephritic syndrome with unspecified morphologic changesBillableN01.ARapidly progressive nephritic syndrome with C3 glomerulonephritisBillable
Related Codes

Frequently Asked Questions

Is N01 a billable ICD-10-CM code?

No, N01 is a non-billable/non-specific code. You should use a more specific sub-code for billing and reimbursement.

What does N01 mean?

N01 is the ICD-10-CM diagnosis code for "Rapidly progressive nephritic syndrome". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What section is N01 in?

N01 is located in Section N00-N08 — "Glomerular diseases" within Chapter 14 of the ICD-10-CM Tabular List.

What are the sub-codes of N01?

N01 has 11 sub-code(s) that provide more specific detail: N01.0, N01.1, N01.2, N01.3, N01.4 and more.

When should I use N01?

Use N01 when the patients documented diagnosis matches "Rapidly progressive nephritic syndrome" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Rapidly progressive nephritic syndrome?

The ICD-10-CM code for Rapidly progressive nephritic syndrome is N01.

Can N01 be used for primary diagnosis?

No, N01 is non-billable. Use a more specific sub-code for primary diagnosis billing.

What chapter is N01 in?

N01 is in Chapter 14 of the ICD-10-CM Tabular List.

What conditions are excluded from N01?

Type 1 Excludes for N01 include: nephritic syndrome NOS (N05.-).

Is N01 valid for 2026?

Yes, N01 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousN00.B2Acute nephritic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)Next →N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormality
Code Details
N01
Rapidly progressive nephritic syndrome
Non-Billable / Non-Specific Code
14 — Diseases of the genitourinary system (N00-N99)
N00-N08 — Glomerular diseases
2026 ICD-10-CM