ICD-10-CM E74.01 is the diagnosis code for von Gierke disease. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.
Understanding where E74.01 sits in the ICD-10-CM classification helps ensure proper coding:
Yes, E74.01 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
E74.01 is the ICD-10-CM diagnosis code for "von Gierke disease". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.
The parent code of E74.01 is E74.0 ("Glycogen storage disease"). E74.01 provides a more specific classification within this category.
E74.01 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.
Use E74.01 when the patients documented diagnosis matches "von Gierke disease" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.
The ICD-10-CM code for von Gierke disease is E74.01.
Yes, E74.01 can be used as a primary diagnosis code since it is billable and specific.
E74.01 is in Chapter 4 of the ICD-10-CM Tabular List.
Yes, E74.01 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.