E75.240
Billable

Niemann-Pick disease type A

Billable / Specific Code

What is Niemann-Pick disease type A?

ICD-10-CM E75.240 is the diagnosis code for Niemann-Pick disease type A. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

💡 Inclusions

Coding Guidelines for E75.240

✅ This Code Includes

  • Acid sphingomyelinase deficiency type A (ASMD type A)
  • Infantile neurovisceral acid sphingomyelinase deficiency

ICD-10-CM Code Hierarchy

Understanding where E75.240 sits in the ICD-10-CM classification helps ensure proper coding:

Related Codes

Frequently Asked Questions

Is E75.240 a billable ICD-10-CM code?

Yes, E75.240 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What does E75.240 mean?

E75.240 is the ICD-10-CM diagnosis code for "Niemann-Pick disease type A". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of E75.240?

The parent code of E75.240 is E75.24 ("Niemann-Pick disease"). E75.240 provides a more specific classification within this category.

What section is E75.240 in?

E75.240 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.

When should I use E75.240?

Use E75.240 when the patients documented diagnosis matches "Niemann-Pick disease type A" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Niemann-Pick disease type A?

The ICD-10-CM code for Niemann-Pick disease type A is E75.240.

Can E75.240 be used for primary diagnosis?

Yes, E75.240 can be used as a primary diagnosis code since it is billable and specific.

What chapter is E75.240 in?

E75.240 is in Chapter 4 of the ICD-10-CM Tabular List.

Is E75.240 valid for 2026?

Yes, E75.240 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousE75.24Niemann-Pick diseaseNext →E75.241Niemann-Pick disease type B
Code Details
E75.240
Niemann-Pick disease type A
Billable / Specific Code
4 — Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 — Metabolic disorders
2026 ICD-10-CM