ICD-10-CM E75.242 is the diagnosis code for Niemann-Pick disease type C. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.
Always refer to the official ICD-10-CM Tabular List for complete coding guidelines. Ensure documentation supports the specificity of the code selected. When in doubt, consult a certified medical coder or the latest CMS guidelines.
Understanding where E75.242 sits in the ICD-10-CM classification helps ensure proper coding:
Yes, E75.242 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
E75.242 is the ICD-10-CM diagnosis code for "Niemann-Pick disease type C". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.
The parent code of E75.242 is E75.24 ("Niemann-Pick disease"). E75.242 provides a more specific classification within this category.
E75.242 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.
Use E75.242 when the patients documented diagnosis matches "Niemann-Pick disease type C" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.
The ICD-10-CM code for Niemann-Pick disease type C is E75.242.
Yes, E75.242 can be used as a primary diagnosis code since it is billable and specific.
E75.242 is in Chapter 4 of the ICD-10-CM Tabular List.
Yes, E75.242 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.