E76.0
Non-Billable

Mucopolysaccharidosis, type I

Non-Billable / Non-Specific Code

What is Mucopolysaccharidosis, type I?

ICD-10-CM E76.0 is the diagnosis code for Mucopolysaccharidosis, type I. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a non-billable/non-specific ICD-10-CM code that should not be used for reimbursement. A more specific sub-code is required for billing. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

Coding Guidelines for E76.0

Always refer to the official ICD-10-CM Tabular List for complete coding guidelines. Ensure documentation supports the specificity of the code selected. When in doubt, consult a certified medical coder or the latest CMS guidelines.

ICD-10-CM Code Hierarchy

Understanding where E76.0 sits in the ICD-10-CM classification helps ensure proper coding:

Sub-Codes 3 entries
E76.01Hurler's syndromeBillableE76.02Hurler-Scheie syndromeBillableE76.03Scheie's syndromeBillable
Related Codes

Frequently Asked Questions

Is E76.0 a billable ICD-10-CM code?

No, E76.0 is a non-billable/non-specific code. You should use a more specific sub-code for billing and reimbursement.

What does E76.0 mean?

E76.0 is the ICD-10-CM diagnosis code for "Mucopolysaccharidosis, type I". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of E76.0?

The parent code of E76.0 is E76 ("Disorders of glycosaminoglycan metabolism"). E76.0 provides a more specific classification within this category.

What section is E76.0 in?

E76.0 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.

What are the sub-codes of E76.0?

E76.0 has 3 sub-code(s) that provide more specific detail: E76.01, E76.02, E76.03.

When should I use E76.0?

Use E76.0 when the patients documented diagnosis matches "Mucopolysaccharidosis, type I" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Mucopolysaccharidosis, type I?

The ICD-10-CM code for Mucopolysaccharidosis, type I is E76.0.

Can E76.0 be used for primary diagnosis?

No, E76.0 is non-billable. Use a more specific sub-code for primary diagnosis billing.

What chapter is E76.0 in?

E76.0 is in Chapter 4 of the ICD-10-CM Tabular List.

Is E76.0 valid for 2026?

Yes, E76.0 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousE76Disorders of glycosaminoglycan metabolismNext →E76.01Hurler's syndrome
Code Details
E76.0
Mucopolysaccharidosis, type I
Non-Billable / Non-Specific Code
4 — Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 — Metabolic disorders
2026 ICD-10-CM