E78.01
Non-Billable

Familial hypercholesterolemia

Non-Billable / Non-Specific Code

What is Familial hypercholesterolemia?

ICD-10-CM E78.01 is the diagnosis code for Familial hypercholesterolemia. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a non-billable/non-specific ICD-10-CM code that should not be used for reimbursement. A more specific sub-code is required for billing. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

Coding Guidelines for E78.01

Always refer to the official ICD-10-CM Tabular List for complete coding guidelines. Ensure documentation supports the specificity of the code selected. When in doubt, consult a certified medical coder or the latest CMS guidelines.

ICD-10-CM Code Hierarchy

Understanding where E78.01 sits in the ICD-10-CM classification helps ensure proper coding:

Sub-Codes 3 entries
E78.010Homozygous familial hypercholesterolemia [HoFH]BillableE78.011Heterozygous familial hypercholesterolemia [HeFH]BillableE78.019Familial hypercholesterolemia, unspecifiedBillable
Related Codes

Frequently Asked Questions

Is E78.01 a billable ICD-10-CM code?

No, E78.01 is a non-billable/non-specific code. You should use a more specific sub-code for billing and reimbursement.

What does E78.01 mean?

E78.01 is the ICD-10-CM diagnosis code for "Familial hypercholesterolemia". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of E78.01?

The parent code of E78.01 is E78.0 ("Pure hypercholesterolemia"). E78.01 provides a more specific classification within this category.

What section is E78.01 in?

E78.01 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.

What are the sub-codes of E78.01?

E78.01 has 3 sub-code(s) that provide more specific detail: E78.010, E78.011, E78.019.

When should I use E78.01?

Use E78.01 when the patients documented diagnosis matches "Familial hypercholesterolemia" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Familial hypercholesterolemia?

The ICD-10-CM code for Familial hypercholesterolemia is E78.01.

Can E78.01 be used for primary diagnosis?

No, E78.01 is non-billable. Use a more specific sub-code for primary diagnosis billing.

What chapter is E78.01 in?

E78.01 is in Chapter 4 of the ICD-10-CM Tabular List.

Is E78.01 valid for 2026?

Yes, E78.01 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousE78.00Pure hypercholesterolemia, unspecifiedNext →E78.010Homozygous familial hypercholesterolemia [HoFH]
Code Details
E78.01
Familial hypercholesterolemia
Non-Billable / Non-Specific Code
4 — Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 — Metabolic disorders
2026 ICD-10-CM