G11.3
Billable

Cerebellar ataxia with defective DNA repair

Billable / Specific Code

What is Cerebellar ataxia with defective DNA repair?

ICD-10-CM G11.3 is the diagnosis code for Cerebellar ataxia with defective DNA repair. This code falls under the section "Systemic atrophies primarily affecting the central nervous system" within Chapter 6 — Diseases of the nervous system (G00-G99). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

💡 Inclusions
â„šī¸ Excludes2

Coding Guidelines for G11.3

✅ This Code Includes

  • Ataxia telangiectasia [Louis-Bar]

â„šī¸ Type 2 Excludes (Code separately if applicable)

The following conditions are not included in G11.3. If the patient has both, code each condition separately:

  • Cockayne's syndrome (Q87.19)
  • other disorders of purine and pyrimidine metabolism (E79.-)
  • xeroderma pigmentosum (Q82.1)

ICD-10-CM Code Hierarchy

Understanding where G11.3 sits in the ICD-10-CM classification helps ensure proper coding:

Related Codes

Frequently Asked Questions

Is G11.3 a billable ICD-10-CM code?

Yes, G11.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What does G11.3 mean?

G11.3 is the ICD-10-CM diagnosis code for "Cerebellar ataxia with defective DNA repair". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of G11.3?

The parent code of G11.3 is G11 ("Hereditary ataxia"). G11.3 provides a more specific classification within this category.

What section is G11.3 in?

G11.3 is located in Section G10-G14 — "Systemic atrophies primarily affecting the central nervous system" within Chapter 6 of the ICD-10-CM Tabular List.

When should I use G11.3?

Use G11.3 when the patients documented diagnosis matches "Cerebellar ataxia with defective DNA repair" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Cerebellar ataxia with defective DNA repair?

The ICD-10-CM code for Cerebellar ataxia with defective DNA repair is G11.3.

Can G11.3 be used for primary diagnosis?

Yes, G11.3 can be used as a primary diagnosis code since it is billable and specific.

What chapter is G11.3 in?

G11.3 is in Chapter 6 of the ICD-10-CM Tabular List.

Is G11.3 valid for 2026?

Yes, G11.3 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousG11.2Late-onset cerebellar ataxiaNext →G11.4Hereditary spastic paraplegia
Code Details
G11.3
Cerebellar ataxia with defective DNA repair
Billable / Specific Code
6 — Diseases of the nervous system (G00-G99)
G10-G14 — Systemic atrophies primarily affecting the central nervous system
2026 ICD-10-CM