Billable / Specific Code
ICD-10-CM G71.3 is the diagnosis code for Mitochondrial myopathy, not elsewhere classified. This code falls under the section "Diseases of myoneural junction and muscle" within Chapter 6 — Diseases of the nervous system (G00-G99). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.
The following conditions should never be coded at the same time as G71.3. They are mutually exclusive:
Understanding where G71.3 sits in the ICD-10-CM classification helps ensure proper coding:
Yes, G71.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
G71.3 is the ICD-10-CM diagnosis code for "Mitochondrial myopathy, not elsewhere classified". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.
The parent code of G71.3 is G71 ("Primary disorders of muscles"). G71.3 provides a more specific classification within this category.
G71.3 is located in Section G70-G73 — "Diseases of myoneural junction and muscle" within Chapter 6 of the ICD-10-CM Tabular List.
Use G71.3 when the patients documented diagnosis matches "Mitochondrial myopathy, not elsewhere classified" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.
The ICD-10-CM code for Mitochondrial myopathy, not elsewhere classified is G71.3.
Yes, G71.3 can be used as a primary diagnosis code since it is billable and specific.
G71.3 is in Chapter 6 of the ICD-10-CM Tabular List.
Type 1 Excludes for G71.3 include: Kearns-Sayre syndrome (H49.81); Leber's disease (H47.21); Leigh's encephalopathy (G31.82) and more.
Yes, G71.3 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.