M04.2
Billable

Cryopyrin-associated periodic syndromes

Billable / Specific Code

What is Cryopyrin-associated periodic syndromes?

ICD-10-CM M04.2 is the diagnosis code for Cryopyrin-associated periodic syndromes. This code falls under the section "Autoinflammatory syndromes" within Chapter 13 — Diseases of the musculoskeletal system and connective tissue (M00-M99). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

💡 Inclusions

Coding Guidelines for M04.2

✅ This Code Includes

  • Chronic infantile neurological, cutaneous and articular syndrome [CINCA]
  • Familial cold autoinflammatory syndrome
  • Familial cold urticaria
  • Muckle-Wells syndrome
  • Neonatal onset multisystemic inflammatory disorder [NOMID]

ICD-10-CM Code Hierarchy

Understanding where M04.2 sits in the ICD-10-CM classification helps ensure proper coding:

Related Codes

Frequently Asked Questions

Is M04.2 a billable ICD-10-CM code?

Yes, M04.2 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What does M04.2 mean?

M04.2 is the ICD-10-CM diagnosis code for "Cryopyrin-associated periodic syndromes". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of M04.2?

The parent code of M04.2 is M04 ("Autoinflammatory syndromes"). M04.2 provides a more specific classification within this category.

What section is M04.2 in?

M04.2 is located in Section M04 — "Autoinflammatory syndromes" within Chapter 13 of the ICD-10-CM Tabular List.

When should I use M04.2?

Use M04.2 when the patients documented diagnosis matches "Cryopyrin-associated periodic syndromes" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Cryopyrin-associated periodic syndromes?

The ICD-10-CM code for Cryopyrin-associated periodic syndromes is M04.2.

Can M04.2 be used for primary diagnosis?

Yes, M04.2 can be used as a primary diagnosis code since it is billable and specific.

What chapter is M04.2 in?

M04.2 is in Chapter 13 of the ICD-10-CM Tabular List.

Is M04.2 valid for 2026?

Yes, M04.2 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousM04.1Periodic fever syndromesNext →M04.8Other autoinflammatory syndromes
Code Details
M04.2
Cryopyrin-associated periodic syndromes
Billable / Specific Code
13 — Diseases of the musculoskeletal system and connective tissue (M00-M99)
M04 — Autoinflammatory syndromes
2026 ICD-10-CM