About Section Q00-Q07

Section Q00-Q07 covers Congenital malformations of the nervous system within Chapter 17 of the ICD-10-CM Tabular List. This section includes diagnosis codes ranging from Q00 to Q07. Each code below includes its description, billable status, and links to detailed coding guidelines.

Diagnosis Codes 53 entries

Q00Anencephaly and similar malformationsNon-Billable›Q00.0AnencephalyBillable›Q00.1CraniorachischisisBillable›Q00.2IniencephalyBillable›Q01EncephaloceleNon-Billable›Q01.0Frontal encephaloceleBillable›Q01.1Nasofrontal encephaloceleBillable›Q01.2Occipital encephaloceleBillable›Q01.8Encephalocele of other sitesBillable›Q01.9Encephalocele, unspecifiedBillable›Q02MicrocephalyBillable›Q03Congenital hydrocephalusNon-Billable›Q03.0Malformations of aqueduct of SylviusBillable›Q03.1Atresia of foramina of Magendie and LuschkaBillable›Q03.8Other congenital hydrocephalusBillable›Q03.9Congenital hydrocephalus, unspecifiedBillable›Q04Other congenital malformations of brainNon-Billable›Q04.0Congenital malformations of corpus callosumBillable›Q04.1ArhinencephalyBillable›Q04.2HoloprosencephalyBillable›Q04.3Other reduction deformities of brainBillable›Q04.4Septo-optic dysplasia of brainBillable›Q04.5MegalencephalyBillable›Q04.6Congenital cerebral cystsBillable›Q04.8Other specified congenital malformations of brainBillable›Q04.9Congenital malformation of brain, unspecifiedBillable›Q05Spina bifidaNon-Billable›Q05.0Cervical spina bifida with hydrocephalusBillable›Q05.1Thoracic spina bifida with hydrocephalusBillable›Q05.2Lumbar spina bifida with hydrocephalusBillable›Q05.3Sacral spina bifida with hydrocephalusBillable›Q05.4Unspecified spina bifida with hydrocephalusBillable›Q05.5Cervical spina bifida without hydrocephalusBillable›Q05.6Thoracic spina bifida without hydrocephalusBillable›Q05.7Lumbar spina bifida without hydrocephalusBillable›Q05.8Sacral spina bifida without hydrocephalusBillable›Q05.9Spina bifida, unspecifiedBillable›Q06Other congenital malformations of spinal cordNon-Billable›Q06.0AmyeliaBillable›Q06.1Hypoplasia and dysplasia of spinal cordBillable›Q06.2DiastematomyeliaBillable›Q06.3Other congenital cauda equina malformationsBillable›Q06.4HydromyeliaBillable›Q06.8Other specified congenital malformations of spinal cordBillable›Q06.9Congenital malformation of spinal cord, unspecifiedBillable›Q07Other congenital malformations of nervous systemNon-Billable›Q07.0Arnold-Chiari syndromeNon-Billable›Q07.00Arnold-Chiari syndrome without spina bifida or hydrocephalusBillable›Q07.01Arnold-Chiari syndrome with spina bifidaBillable›Q07.02Arnold-Chiari syndrome with hydrocephalusBillable›Q07.03Arnold-Chiari syndrome with spina bifida and hydrocephalusBillable›Q07.8Other specified congenital malformations of nervous systemBillable›Q07.9Congenital malformation of nervous system, unspecifiedBillable›