D81.818
Billable

Other biotin-dependent carboxylase deficiency

Billable / Specific Code

What is Other biotin-dependent carboxylase deficiency?

ICD-10-CM D81.818 is the diagnosis code for Other biotin-dependent carboxylase deficiency. This code falls under the section "Certain disorders involving the immune mechanism" within Chapter 3 — Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

💡 Inclusions

Coding Guidelines for D81.818

✅ This Code Includes

  • Holocarboxylase synthetase deficiency
  • Other multiple carboxylase deficiency

ICD-10-CM Code Hierarchy

Understanding where D81.818 sits in the ICD-10-CM classification helps ensure proper coding:

Related Codes

Frequently Asked Questions

Is D81.818 a billable ICD-10-CM code?

Yes, D81.818 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What does D81.818 mean?

D81.818 is the ICD-10-CM diagnosis code for "Other biotin-dependent carboxylase deficiency". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of D81.818?

The parent code of D81.818 is D81.81 ("Biotin-dependent carboxylase deficiency"). D81.818 provides a more specific classification within this category.

What section is D81.818 in?

D81.818 is located in Section D80-D89 — "Certain disorders involving the immune mechanism" within Chapter 3 of the ICD-10-CM Tabular List.

When should I use D81.818?

Use D81.818 when the patients documented diagnosis matches "Other biotin-dependent carboxylase deficiency" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Other biotin-dependent carboxylase deficiency?

The ICD-10-CM code for Other biotin-dependent carboxylase deficiency is D81.818.

Can D81.818 be used for primary diagnosis?

Yes, D81.818 can be used as a primary diagnosis code since it is billable and specific.

What chapter is D81.818 in?

D81.818 is in Chapter 3 of the ICD-10-CM Tabular List.

Is D81.818 valid for 2026?

Yes, D81.818 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousD81.810Biotinidase deficiencyNext →D81.819Biotin-dependent carboxylase deficiency, unspecified
Code Details
D81.818
Other biotin-dependent carboxylase deficiency
Billable / Specific Code
3 — Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D80-D89 — Certain disorders involving the immune mechanism
2026 ICD-10-CM