About Section D80-D89

Section D80-D89 covers Certain disorders involving the immune mechanism within Chapter 3 of the ICD-10-CM Tabular List. This section includes diagnosis codes ranging from D80 to D89. Each code below includes its description, billable status, and links to detailed coding guidelines.
Diagnosis Codes 100 entries
D80Immunodeficiency with predominantly antibody defectsNon-Billable›D80.0Hereditary hypogammaglobulinemiaBillable›D80.1Nonfamilial hypogammaglobulinemiaBillable›D80.2Selective deficiency of immunoglobulin A [IgA]Billable›D80.3Selective deficiency of immunoglobulin G [IgG] subclassesBillable›D80.4Selective deficiency of immunoglobulin M [IgM]Billable›D80.5Immunodeficiency with increased immunoglobulin M [IgM]Billable›D80.6Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemiaBillable›D80.7Transient hypogammaglobulinemia of infancyBillable›D80.8Other immunodeficiencies with predominantly antibody defectsBillable›D80.9Immunodeficiency with predominantly antibody defects, unspecifiedBillable›D81Combined immunodeficienciesNon-Billable›D81.0Severe combined immunodeficiency [SCID] with reticular dysgenesisBillable›D81.1Severe combined immunodeficiency [SCID] with low T- and B-cell numbersBillable›D81.2Severe combined immunodeficiency [SCID] with low or normal B-cell numbersBillable›D81.3Adenosine deaminase [ADA] deficiencyNon-Billable›D81.30Adenosine deaminase deficiency, unspecifiedBillable›D81.31Severe combined immunodeficiency due to adenosine deaminase deficiencyBillable›D81.32Adenosine deaminase 2 deficiencyBillable›D81.39Other adenosine deaminase deficiencyBillable›D81.4Nezelof's syndromeBillable›D81.5Purine nucleoside phosphorylase [PNP] deficiencyBillable›D81.6Major histocompatibility complex class I deficiencyBillable›D81.7Major histocompatibility complex class II deficiencyBillable›D81.8Other combined immunodeficienciesNon-Billable›D81.81Biotin-dependent carboxylase deficiencyNon-Billable›D81.810Biotinidase deficiencyBillable›D81.818Other biotin-dependent carboxylase deficiencyBillable›D81.819Biotin-dependent carboxylase deficiency, unspecifiedBillable›D81.82Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]Billable›D81.89Other combined immunodeficienciesBillable›D81.9Combined immunodeficiency, unspecifiedBillable›D82Immunodeficiency associated with other major defectsNon-Billable›D82.0Wiskott-Aldrich syndromeBillable›D82.1Di George's syndromeBillable›D82.2Immunodeficiency with short-limbed statureBillable›D82.3Immunodeficiency following hereditary defective response to Epstein-Barr virusBillable›D82.4Hyperimmunoglobulin E [IgE] syndromeBillable›D82.8Immunodeficiency associated with other specified major defectsBillable›D82.9Immunodeficiency associated with major defect, unspecifiedBillable›D83Common variable immunodeficiencyNon-Billable›D83.0Common variable immunodeficiency with predominant abnormalities of B-cell numbers and functionBillable›D83.1Common variable immunodeficiency with predominant immunoregulatory T-cell disordersBillable›D83.2Common variable immunodeficiency with autoantibodies to B- or T-cellsBillable›D83.8Other common variable immunodeficienciesBillable›D83.9Common variable immunodeficiency, unspecifiedBillable›D84Other immunodeficienciesNon-Billable›D84.0Lymphocyte function antigen-1 [LFA-1] defectBillable›D84.1Defects in the complement systemBillable›D84.8Other specified immunodeficienciesNon-Billable›D84.81Immunodeficiency due to conditions classified elsewhereBillable›D84.82Immunodeficiency due to drugs and external causesNon-Billable›D84.821Immunodeficiency due to drugsBillable›D84.822Immunodeficiency due to external causesBillable›D84.89Other immunodeficienciesBillable›D84.9Immunodeficiency, unspecifiedBillable›D86SarcoidosisNon-Billable›D86.0Sarcoidosis of lungBillable›D86.1Sarcoidosis of lymph nodesBillable›D86.2Sarcoidosis of lung with sarcoidosis of lymph nodesBillable›D86.3Sarcoidosis of skinBillable›D86.8Sarcoidosis of other sitesNon-Billable›D86.81Sarcoid meningitisBillable›D86.82Multiple cranial nerve palsies in sarcoidosisBillable›D86.83Sarcoid iridocyclitisBillable›D86.84Sarcoid pyelonephritisBillable›D86.85Sarcoid myocarditisBillable›D86.86Sarcoid arthropathyBillable›D86.87Sarcoid myositisBillable›D86.89Sarcoidosis of other sitesBillable›D86.9Sarcoidosis, unspecifiedBillable›D89Other disorders involving the immune mechanism, not elsewhere classifiedNon-Billable›D89.0Polyclonal hypergammaglobulinemiaBillable›D89.1CryoglobulinemiaBillable›D89.2Hypergammaglobulinemia, unspecifiedBillable›D89.3Immune reconstitution syndromeBillable›D89.4Mast cell activation syndrome and related disordersNon-Billable›D89.40Mast cell activation, unspecifiedBillable›D89.41Monoclonal mast cell activation syndromeBillable›D89.42Idiopathic mast cell activation syndromeBillable›D89.43Secondary mast cell activationBillable›D89.44Hereditary alpha tryptasemiaBillable›D89.49Other mast cell activation disorderBillable›D89.8Other specified disorders involving the immune mechanism, not elsewhere classifiedNon-Billable›D89.81Graft-versus-host diseaseNon-Billable›D89.810Acute graft-versus-host diseaseBillable›D89.811Chronic graft-versus-host diseaseBillable›D89.812Acute on chronic graft-versus-host diseaseBillable›D89.813Graft-versus-host disease, unspecifiedBillable›D89.82Autoimmune lymphoproliferative syndrome [ALPS]Billable›D89.83Cytokine release syndromeNon-Billable›D89.831Cytokine release syndrome, grade 1Billable›D89.832Cytokine release syndrome, grade 2Billable›D89.833Cytokine release syndrome, grade 3Billable›D89.834Cytokine release syndrome, grade 4Billable›D89.835Cytokine release syndrome, grade 5Billable›D89.839Cytokine release syndrome, grade unspecifiedBillable›D89.84IgG4-related diseaseBillable›D89.89Other specified disorders involving the immune mechanism, not elsewhere classifiedBillable›D89.9Disorder involving the immune mechanism, unspecifiedBillable›