D89.42
Billable

Idiopathic mast cell activation syndrome

Billable / Specific Code

What is Idiopathic mast cell activation syndrome?

ICD-10-CM D89.42 is the diagnosis code for Idiopathic mast cell activation syndrome. This code falls under the section "Certain disorders involving the immune mechanism" within Chapter 3 — Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

Coding Guidelines for D89.42

Always refer to the official ICD-10-CM Tabular List for complete coding guidelines. Ensure documentation supports the specificity of the code selected. When in doubt, consult a certified medical coder or the latest CMS guidelines.

ICD-10-CM Code Hierarchy

Understanding where D89.42 sits in the ICD-10-CM classification helps ensure proper coding:

Related Codes

Frequently Asked Questions

Is D89.42 a billable ICD-10-CM code?

Yes, D89.42 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What does D89.42 mean?

D89.42 is the ICD-10-CM diagnosis code for "Idiopathic mast cell activation syndrome". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of D89.42?

The parent code of D89.42 is D89.4 ("Mast cell activation syndrome and related disorders"). D89.42 provides a more specific classification within this category.

What section is D89.42 in?

D89.42 is located in Section D80-D89 — "Certain disorders involving the immune mechanism" within Chapter 3 of the ICD-10-CM Tabular List.

When should I use D89.42?

Use D89.42 when the patients documented diagnosis matches "Idiopathic mast cell activation syndrome" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Idiopathic mast cell activation syndrome?

The ICD-10-CM code for Idiopathic mast cell activation syndrome is D89.42.

Can D89.42 be used for primary diagnosis?

Yes, D89.42 can be used as a primary diagnosis code since it is billable and specific.

What chapter is D89.42 in?

D89.42 is in Chapter 3 of the ICD-10-CM Tabular List.

Is D89.42 valid for 2026?

Yes, D89.42 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousD89.41Monoclonal mast cell activation syndromeNext →D89.43Secondary mast cell activation
Code Details
D89.42
Idiopathic mast cell activation syndrome
Billable / Specific Code
3 — Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D80-D89 — Certain disorders involving the immune mechanism
2026 ICD-10-CM