D89.4
Non-Billable

Mast cell activation syndrome and related disorders

Non-Billable / Non-Specific Code

What is Mast cell activation syndrome and related disorders?

ICD-10-CM D89.4 is the diagnosis code for Mast cell activation syndrome and related disorders. This code falls under the section "Certain disorders involving the immune mechanism" within Chapter 3 — Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89). It is a non-billable/non-specific ICD-10-CM code that should not be used for reimbursement. A more specific sub-code is required for billing. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

⛔ Excludes1

Coding Guidelines for D89.4

⛔ Type 1 Excludes (Never code together)

The following conditions should never be coded at the same time as D89.4. They are mutually exclusive:

  • aggressive systemic mastocytosis (C96.21)
  • congenital cutaneous mastocytosis (Q82.2)
  • (non-congenital) cutaneous mastocytosis (D47.01)
  • (indolent) systemic mastocytosis (D47.02)
  • malignant mast cell neoplasm (C96.2-)
  • malignant mastocytoma (C96.29)
  • mast cell leukemia (C94.3-)
  • mast cell sarcoma (C96.22)
  • mastocytoma NOS (D47.09)
  • other mast cell neoplasms of uncertain behavior (D47.09)
  • systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02)

ICD-10-CM Code Hierarchy

Understanding where D89.4 sits in the ICD-10-CM classification helps ensure proper coding:

Sub-Codes 6 entries
D89.40Mast cell activation, unspecifiedBillableD89.41Monoclonal mast cell activation syndromeBillableD89.42Idiopathic mast cell activation syndromeBillableD89.43Secondary mast cell activationBillableD89.44Hereditary alpha tryptasemiaBillableD89.49Other mast cell activation disorderBillable
Related Codes

Frequently Asked Questions

Is D89.4 a billable ICD-10-CM code?

No, D89.4 is a non-billable/non-specific code. You should use a more specific sub-code for billing and reimbursement.

What does D89.4 mean?

D89.4 is the ICD-10-CM diagnosis code for "Mast cell activation syndrome and related disorders". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of D89.4?

The parent code of D89.4 is D89 ("Other disorders involving the immune mechanism, not elsewhere classified"). D89.4 provides a more specific classification within this category.

What section is D89.4 in?

D89.4 is located in Section D80-D89 — "Certain disorders involving the immune mechanism" within Chapter 3 of the ICD-10-CM Tabular List.

What are the sub-codes of D89.4?

D89.4 has 6 sub-code(s) that provide more specific detail: D89.40, D89.41, D89.42, D89.43, D89.44 and more.

When should I use D89.4?

Use D89.4 when the patients documented diagnosis matches "Mast cell activation syndrome and related disorders" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Mast cell activation syndrome and related disorders?

The ICD-10-CM code for Mast cell activation syndrome and related disorders is D89.4.

Can D89.4 be used for primary diagnosis?

No, D89.4 is non-billable. Use a more specific sub-code for primary diagnosis billing.

What chapter is D89.4 in?

D89.4 is in Chapter 3 of the ICD-10-CM Tabular List.

What conditions are excluded from D89.4?

Type 1 Excludes for D89.4 include: aggressive systemic mastocytosis (C96.21); congenital cutaneous mastocytosis (Q82.2); (non-congenital) cutaneous mastocytosis (D47.01) and more.

Is D89.4 valid for 2026?

Yes, D89.4 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousD89.3Immune reconstitution syndromeNext →D89.40Mast cell activation, unspecified
Code Details
D89.4
Mast cell activation syndrome and related disorders
Non-Billable / Non-Specific Code
3 — Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
D80-D89 — Certain disorders involving the immune mechanism
2026 ICD-10-CM