ICD-10-CM E76.1 is the diagnosis code for Mucopolysaccharidosis, type II. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.
Understanding where E76.1 sits in the ICD-10-CM classification helps ensure proper coding:
Yes, E76.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
E76.1 is the ICD-10-CM diagnosis code for "Mucopolysaccharidosis, type II". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.
The parent code of E76.1 is E76 ("Disorders of glycosaminoglycan metabolism"). E76.1 provides a more specific classification within this category.
E76.1 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.
Use E76.1 when the patients documented diagnosis matches "Mucopolysaccharidosis, type II" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.
The ICD-10-CM code for Mucopolysaccharidosis, type II is E76.1.
Yes, E76.1 can be used as a primary diagnosis code since it is billable and specific.
E76.1 is in Chapter 4 of the ICD-10-CM Tabular List.
Yes, E76.1 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.