E78.010
Billable

Homozygous familial hypercholesterolemia [HoFH]

Billable / Specific Code

What is Homozygous familial hypercholesterolemia [HoFH]?

ICD-10-CM E78.010 is the diagnosis code for Homozygous familial hypercholesterolemia [HoFH]. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

Coding Guidelines for E78.010

Always refer to the official ICD-10-CM Tabular List for complete coding guidelines. Ensure documentation supports the specificity of the code selected. When in doubt, consult a certified medical coder or the latest CMS guidelines.

ICD-10-CM Code Hierarchy

Understanding where E78.010 sits in the ICD-10-CM classification helps ensure proper coding:

Current CodeE78.010 — Homozygous familial hypercholesterolemia [HoFH]
Related Codes

Frequently Asked Questions

Is E78.010 a billable ICD-10-CM code?

Yes, E78.010 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What does E78.010 mean?

E78.010 is the ICD-10-CM diagnosis code for "Homozygous familial hypercholesterolemia [HoFH]". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of E78.010?

The parent code of E78.010 is E78.01 ("Familial hypercholesterolemia"). E78.010 provides a more specific classification within this category.

What section is E78.010 in?

E78.010 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.

When should I use E78.010?

Use E78.010 when the patients documented diagnosis matches "Homozygous familial hypercholesterolemia [HoFH]" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Homozygous familial hypercholesterolemia [HoFH]?

The ICD-10-CM code for Homozygous familial hypercholesterolemia [HoFH] is E78.010.

Can E78.010 be used for primary diagnosis?

Yes, E78.010 can be used as a primary diagnosis code since it is billable and specific.

What chapter is E78.010 in?

E78.010 is in Chapter 4 of the ICD-10-CM Tabular List.

Is E78.010 valid for 2026?

Yes, E78.010 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousE78.01Familial hypercholesterolemiaNext →E78.011Heterozygous familial hypercholesterolemia [HeFH]
Code Details
E78.010
Homozygous familial hypercholesterolemia [HoFH]
Billable / Specific Code
4 — Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 — Metabolic disorders
2026 ICD-10-CM