E88.43
Billable

Disorders of mitochondrial tRNA synthetases

Billable / Specific Code

What is Disorders of mitochondrial tRNA synthetases?

ICD-10-CM E88.43 is the diagnosis code for Disorders of mitochondrial tRNA synthetases. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

💡 Inclusions

Coding Guidelines for E88.43

✅ This Code Includes

  • ARS2-related mitochondrial disorders
  • LBSL
  • Leukoencephalopathy with brainstem - spinal cord involvement - lactate elevation
  • Leukoencephalopathy with thalamus - brainstem involvement - high lactate
  • LTBL
  • Mitochondrial aminoacyl-tRNA synthetase disorders

ICD-10-CM Code Hierarchy

Understanding where E88.43 sits in the ICD-10-CM classification helps ensure proper coding:

Current CodeE88.43 — Disorders of mitochondrial tRNA synthetases
Related Codes

Frequently Asked Questions

Is E88.43 a billable ICD-10-CM code?

Yes, E88.43 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What does E88.43 mean?

E88.43 is the ICD-10-CM diagnosis code for "Disorders of mitochondrial tRNA synthetases". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of E88.43?

The parent code of E88.43 is E88.4 ("Mitochondrial metabolism disorders"). E88.43 provides a more specific classification within this category.

What section is E88.43 in?

E88.43 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.

When should I use E88.43?

Use E88.43 when the patients documented diagnosis matches "Disorders of mitochondrial tRNA synthetases" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Disorders of mitochondrial tRNA synthetases?

The ICD-10-CM code for Disorders of mitochondrial tRNA synthetases is E88.43.

Can E88.43 be used for primary diagnosis?

Yes, E88.43 can be used as a primary diagnosis code since it is billable and specific.

What chapter is E88.43 in?

E88.43 is in Chapter 4 of the ICD-10-CM Tabular List.

Is E88.43 valid for 2026?

Yes, E88.43 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousE88.42MERRF syndromeNext →E88.49Other mitochondrial metabolism disorders
Code Details
E88.43
Disorders of mitochondrial tRNA synthetases
Billable / Specific Code
4 — Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 — Metabolic disorders
2026 ICD-10-CM