M04.1
Billable

Periodic fever syndromes

Billable / Specific Code

What is Periodic fever syndromes?

ICD-10-CM M04.1 is the diagnosis code for Periodic fever syndromes. This code falls under the section "Autoinflammatory syndromes" within Chapter 13 — Diseases of the musculoskeletal system and connective tissue (M00-M99). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

💡 Inclusions

Coding Guidelines for M04.1

✅ This Code Includes

  • Familial Mediterranean fever
  • Hyperimmunoglobin D syndrome
  • Mevalonate kinase deficiency
  • Tumor necrosis factor receptor associated periodic syndrome [TRAPS]

ICD-10-CM Code Hierarchy

Understanding where M04.1 sits in the ICD-10-CM classification helps ensure proper coding:

Related Codes

Frequently Asked Questions

Is M04.1 a billable ICD-10-CM code?

Yes, M04.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What does M04.1 mean?

M04.1 is the ICD-10-CM diagnosis code for "Periodic fever syndromes". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of M04.1?

The parent code of M04.1 is M04 ("Autoinflammatory syndromes"). M04.1 provides a more specific classification within this category.

What section is M04.1 in?

M04.1 is located in Section M04 — "Autoinflammatory syndromes" within Chapter 13 of the ICD-10-CM Tabular List.

When should I use M04.1?

Use M04.1 when the patients documented diagnosis matches "Periodic fever syndromes" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Periodic fever syndromes?

The ICD-10-CM code for Periodic fever syndromes is M04.1.

Can M04.1 be used for primary diagnosis?

Yes, M04.1 can be used as a primary diagnosis code since it is billable and specific.

What chapter is M04.1 in?

M04.1 is in Chapter 13 of the ICD-10-CM Tabular List.

Is M04.1 valid for 2026?

Yes, M04.1 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousM04Autoinflammatory syndromesNext →M04.2Cryopyrin-associated periodic syndromes
Code Details
M04.1
Periodic fever syndromes
Billable / Specific Code
13 — Diseases of the musculoskeletal system and connective tissue (M00-M99)
M04 — Autoinflammatory syndromes
2026 ICD-10-CM