ICD-10-CM Q81.0 is the diagnosis code for Epidermolysis bullosa simplex. This code falls under the section "Other congenital malformations" within Chapter 17 — Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.
The following conditions should never be coded at the same time as Q81.0. They are mutually exclusive:
Understanding where Q81.0 sits in the ICD-10-CM classification helps ensure proper coding:
Yes, Q81.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
Q81.0 is the ICD-10-CM diagnosis code for "Epidermolysis bullosa simplex". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.
The parent code of Q81.0 is Q81 ("Epidermolysis bullosa"). Q81.0 provides a more specific classification within this category.
Q81.0 is located in Section Q80-Q89 — "Other congenital malformations" within Chapter 17 of the ICD-10-CM Tabular List.
Use Q81.0 when the patients documented diagnosis matches "Epidermolysis bullosa simplex" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.
The ICD-10-CM code for Epidermolysis bullosa simplex is Q81.0.
Yes, Q81.0 can be used as a primary diagnosis code since it is billable and specific.
Q81.0 is in Chapter 17 of the ICD-10-CM Tabular List.
Type 1 Excludes for Q81.0 include: Cockayne's syndrome (Q87.19).
Yes, Q81.0 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.