About Section Q80-Q89

Section Q80-Q89 covers Other congenital malformations within Chapter 17 of the ICD-10-CM Tabular List. This section includes diagnosis codes ranging from Q80 to Q89. Each code below includes its description, billable status, and links to detailed coding guidelines.
Diagnosis Codes 98 entries
Q80Congenital ichthyosisNon-Billable›Q80.0Ichthyosis vulgarisBillable›Q80.1X-linked ichthyosisBillable›Q80.2Lamellar ichthyosisBillable›Q80.3Congenital bullous ichthyosiform erythrodermaBillable›Q80.4Harlequin fetusBillable›Q80.8Other congenital ichthyosisBillable›Q80.9Congenital ichthyosis, unspecifiedBillable›Q81Epidermolysis bullosaNon-Billable›Q81.0Epidermolysis bullosa simplexBillable›Q81.1Epidermolysis bullosa letalisBillable›Q81.2Epidermolysis bullosa dystrophicaBillable›Q81.8Other epidermolysis bullosaBillable›Q81.9Epidermolysis bullosa, unspecifiedBillable›Q82Other congenital malformations of skinNon-Billable›Q82.0Hereditary lymphedemaBillable›Q82.1Xeroderma pigmentosumBillable›Q82.2Congenital cutaneous mastocytosisBillable›Q82.3Incontinentia pigmentiBillable›Q82.4Ectodermal dysplasia (anhidrotic)Billable›Q82.5Congenital non-neoplastic nevusBillable›Q82.6Congenital sacral dimpleBillable›Q82.8Other specified congenital malformations of skinBillable›Q82.9Congenital malformation of skin, unspecifiedBillable›Q83Congenital malformations of breastNon-Billable›Q83.0Congenital absence of breast with absent nippleBillable›Q83.1Accessory breastBillable›Q83.2Absent nippleBillable›Q83.3Accessory nippleBillable›Q83.8Other congenital malformations of breastBillable›Q83.9Congenital malformation of breast, unspecifiedBillable›Q84Other congenital malformations of integumentNon-Billable›Q84.0Congenital alopeciaBillable›Q84.1Congenital morphological disturbances of hair, not elsewhere classifiedBillable›Q84.2Other congenital malformations of hairBillable›Q84.3AnonychiaBillable›Q84.4Congenital leukonychiaBillable›Q84.5Enlarged and hypertrophic nailsBillable›Q84.6Other congenital malformations of nailsBillable›Q84.8Other specified congenital malformations of integumentBillable›Q84.9Congenital malformation of integument, unspecifiedBillable›Q85Phakomatoses, not elsewhere classifiedNon-Billable›Q85.0Neurofibromatosis (nonmalignant)Non-Billable›Q85.00Neurofibromatosis, unspecifiedBillable›Q85.01Neurofibromatosis, type 1Billable›Q85.02Neurofibromatosis, type 2Billable›Q85.03SchwannomatosisBillable›Q85.09Other neurofibromatosisBillable›Q85.1Tuberous sclerosisBillable›Q85.8Other phakomatoses, not elsewhere classifiedNon-Billable›Q85.81PTEN hamartoma tumor syndromeBillable›Q85.82Other Cowden syndromeBillable›Q85.83Von Hippel-Lindau syndromeBillable›Q85.89Other phakomatoses, not elsewhere classifiedBillable›Q85.9Phakomatosis, unspecifiedBillable›Q86Congenital malformation syndromes due to known exogenous causes, not elsewhere classifiedNon-Billable›Q86.0Fetal alcohol syndrome (dysmorphic)Billable›Q86.1Fetal hydantoin syndromeBillable›Q86.2Dysmorphism due to warfarinBillable›Q86.8Other congenital malformation syndromes due to known exogenous causesBillable›Q87Other specified congenital malformation syndromes affecting multiple systemsNon-Billable›Q87.0Congenital malformation syndromes predominantly affecting facial appearanceBillable›Q87.1Congenital malformation syndromes predominantly associated with short statureNon-Billable›Q87.11Prader-Willi syndromeBillable›Q87.19Other congenital malformation syndromes predominantly associated with short statureBillable›Q87.2Congenital malformation syndromes predominantly involving limbsBillable›Q87.3Congenital malformation syndromes involving early overgrowthBillable›Q87.4Marfan syndromeNon-Billable›Q87.40Marfan syndrome, unspecifiedBillable›Q87.41Marfan syndrome with cardiovascular manifestationsNon-Billable›Q87.410Marfan syndrome with aortic dilationBillable›Q87.418Marfan syndrome with other cardiovascular manifestationsBillable›Q87.42Marfan syndrome with ocular manifestationsBillable›Q87.43Marfan syndrome with skeletal manifestationBillable›Q87.5Other congenital malformation syndromes with other skeletal changesBillable›Q87.8Other specified congenital malformation syndromes, not elsewhere classifiedNon-Billable›Q87.81Alport syndromeBillable›Q87.82Arterial tortuosity syndromeBillable›Q87.83Bardet-Biedl syndromeBillable›Q87.84Laurence-Moon syndromeBillable›Q87.85MED13L syndromeBillable›Q87.86Kleefstra syndromeBillable›Q87.87Hao-Fountain SyndromeBillable›Q87.88CTNNB1 syndromeBillable›Q87.89Other specified congenital malformation syndromes, not elsewhere classifiedBillable›Q89Other congenital malformations, not elsewhere classifiedNon-Billable›Q89.0Congenital absence and malformations of spleenNon-Billable›Q89.01Asplenia (congenital)Billable›Q89.09Congenital malformations of spleenBillable›Q89.1Congenital malformations of adrenal glandBillable›Q89.2Congenital malformations of other endocrine glandsBillable›Q89.3Situs inversusBillable›Q89.4Conjoined twinsBillable›Q89.7Multiple congenital malformations, not elsewhere classifiedBillable›Q89.8Other specified congenital malformationsNon-Billable›Q89.81Kabuki syndromeBillable›Q89.89Other specified congenital malformationsBillable›Q89.9Congenital malformation, unspecifiedBillable›