ICD-10-CM Q89.81 is the diagnosis code for Kabuki syndrome. This code falls under the section "Other congenital malformations" within Chapter 17 — Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.
Understanding where Q89.81 sits in the ICD-10-CM classification helps ensure proper coding:
Yes, Q89.81 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
Q89.81 is the ICD-10-CM diagnosis code for "Kabuki syndrome". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.
The parent code of Q89.81 is Q89.8 ("Other specified congenital malformations"). Q89.81 provides a more specific classification within this category.
Q89.81 is located in Section Q80-Q89 — "Other congenital malformations" within Chapter 17 of the ICD-10-CM Tabular List.
Use Q89.81 when the patients documented diagnosis matches "Kabuki syndrome" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.
The ICD-10-CM code for Kabuki syndrome is Q89.81.
Yes, Q89.81 can be used as a primary diagnosis code since it is billable and specific.
Q89.81 is in Chapter 17 of the ICD-10-CM Tabular List.
Yes, Q89.81 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.