About Section M30-M36

Section M30-M36 covers Systemic connective tissue disorders within Chapter 13 of the ICD-10-CM Tabular List. This section includes diagnosis codes ranging from M30 to M36. Each code below includes its description, billable status, and links to detailed coding guidelines.
Diagnosis Codes 101 entries
M30Polyarteritis nodosa and related conditionsNon-Billable›M30.0Polyarteritis nodosaBillable›M30.1Polyarteritis with lung involvement [Churg-Strauss]Billable›M30.2Juvenile polyarteritisBillable›M30.3Mucocutaneous lymph node syndrome [Kawasaki]Billable›M30.8Other conditions related to polyarteritis nodosaBillable›M31Other necrotizing vasculopathiesNon-Billable›M31.0Hypersensitivity angiitisBillable›M31.1Thrombotic microangiopathyNon-Billable›M31.10Thrombotic microangiopathy, unspecifiedBillable›M31.11Hematopoietic stem cell transplantation-associated thrombotic microangiopathy [HSCT-TMA]Billable›M31.19Other thrombotic microangiopathyBillable›M31.2Lethal midline granulomaBillable›M31.3Wegener's granulomatosisNon-Billable›M31.30Wegener's granulomatosis without renal involvementBillable›M31.31Wegener's granulomatosis with renal involvementBillable›M31.4Aortic arch syndrome [Takayasu]Billable›M31.5Giant cell arteritis with polymyalgia rheumaticaBillable›M31.6Other giant cell arteritisBillable›M31.7Microscopic polyangiitisBillable›M31.8Other specified necrotizing vasculopathiesBillable›M31.9Necrotizing vasculopathy, unspecifiedBillable›M32Systemic lupus erythematosus (SLE)Non-Billable›M32.0Drug-induced systemic lupus erythematosusBillable›M32.1Systemic lupus erythematosus with organ or system involvementNon-Billable›M32.10Systemic lupus erythematosus, organ or system involvement unspecifiedBillable›M32.11Endocarditis in systemic lupus erythematosusBillable›M32.12Pericarditis in systemic lupus erythematosusBillable›M32.13Lung involvement in systemic lupus erythematosusBillable›M32.14Glomerular disease in systemic lupus erythematosusBillable›M32.15Tubulo-interstitial nephropathy in systemic lupus erythematosusBillable›M32.19Other organ or system involvement in systemic lupus erythematosusBillable›M32.8Other forms of systemic lupus erythematosusBillable›M32.9Systemic lupus erythematosus, unspecifiedBillable›M33DermatopolymyositisNon-Billable›M33.0Juvenile dermatomyositisNon-Billable›M33.00Juvenile dermatomyositis, organ involvement unspecifiedBillable›M33.01Juvenile dermatomyositis with respiratory involvementBillable›M33.02Juvenile dermatomyositis with myopathyBillable›M33.03Juvenile dermatomyositis without myopathyBillable›M33.09Juvenile dermatomyositis with other organ involvementBillable›M33.1Other dermatomyositisNon-Billable›M33.10Other dermatomyositis, organ involvement unspecifiedBillable›M33.11Other dermatomyositis with respiratory involvementBillable›M33.12Other dermatomyositis with myopathyBillable›M33.13Other dermatomyositis without myopathyBillable›M33.19Other dermatomyositis with other organ involvementBillable›M33.2PolymyositisNon-Billable›M33.20Polymyositis, organ involvement unspecifiedBillable›M33.21Polymyositis with respiratory involvementBillable›M33.22Polymyositis with myopathyBillable›M33.29Polymyositis with other organ involvementBillable›M33.9Dermatopolymyositis, unspecifiedNon-Billable›M33.90Dermatopolymyositis, unspecified, organ involvement unspecifiedBillable›M33.91Dermatopolymyositis, unspecified with respiratory involvementBillable›M33.92Dermatopolymyositis, unspecified with myopathyBillable›M33.93Dermatopolymyositis, unspecified without myopathyBillable›M33.99Dermatopolymyositis, unspecified with other organ involvementBillable›M34Systemic sclerosis [scleroderma]Non-Billable›M34.0Progressive systemic sclerosisBillable›M34.1CR(E)ST syndromeBillable›M34.2Systemic sclerosis induced by drug and chemicalBillable›M34.8Other forms of systemic sclerosisNon-Billable›M34.81Systemic sclerosis with lung involvementBillable›M34.82Systemic sclerosis with myopathyBillable›M34.83Systemic sclerosis with polyneuropathyBillable›M34.89Other systemic sclerosisBillable›M34.9Systemic sclerosis, unspecifiedBillable›M35Other systemic involvement of connective tissueNon-Billable›M35.0Sjögren syndromeNon-Billable›M35.00Sjögren syndrome, unspecifiedBillable›M35.01Sjögren syndrome with keratoconjunctivitisBillable›M35.02Sjögren syndrome with lung involvementBillable›M35.03Sjögren syndrome with myopathyBillable›M35.04Sjögren syndrome with tubulo-interstitial nephropathyBillable›M35.05Sjögren syndrome with inflammatory arthritisBillable›M35.06Sjögren syndrome with peripheral nervous system involvementBillable›M35.07Sjögren syndrome with central nervous system involvementBillable›M35.08Sjögren syndrome with gastrointestinal involvementBillable›M35.09Sjögren syndrome with other organ involvementBillable›M35.0ASjögren syndrome with glomerular diseaseBillable›M35.0BSjögren syndrome with vasculitisBillable›M35.0CSjögren syndrome with dental involvementBillable›M35.1Other overlap syndromesBillable›M35.2Behçet's diseaseBillable›M35.3Polymyalgia rheumaticaBillable›M35.4Diffuse (eosinophilic) fasciitisBillable›M35.5Multifocal fibrosclerosisBillable›M35.6Relapsing panniculitis [Weber-Christian]Billable›M35.7Hypermobility syndromeBillable›M35.8Other specified systemic involvement of connective tissueNon-Billable›M35.81Multisystem inflammatory syndromeBillable›M35.89Other specified systemic involvement of connective tissueBillable›M35.9Systemic involvement of connective tissue, unspecifiedBillable›M36Systemic disorders of connective tissue in diseases classified elsewhereNon-Billable›M36.0Dermato(poly)myositis in neoplastic diseaseBillable›M36.1Arthropathy in neoplastic diseaseBillable›M36.2Hemophilic arthropathyBillable›M36.3Arthropathy in other blood disordersBillable›M36.4Arthropathy in hypersensitivity reactions classified elsewhereBillable›M36.8Systemic disorders of connective tissue in other diseases classified elsewhereBillable›