E75
Non-Billable

Disorders of sphingolipid metabolism and other lipid storage disorders

Non-Billable / Non-Specific Code

What is Disorders of sphingolipid metabolism and other lipid storage disorders?

ICD-10-CM E75 is the diagnosis code for Disorders of sphingolipid metabolism and other lipid storage disorders. This code falls under the section "Metabolic disorders" within Chapter 4 — Endocrine, nutritional and metabolic diseases (E00-E89). It is a non-billable/non-specific ICD-10-CM code that should not be used for reimbursement. A more specific sub-code is required for billing. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

⛔ Excludes1

Coding Guidelines for E75

⛔ Type 1 Excludes (Never code together)

The following conditions should never be coded at the same time as E75. They are mutually exclusive:

  • mucolipidosis, types I-III (E77.0-E77.1)
  • Refsum's disease (G60.1)

ICD-10-CM Code Hierarchy

Understanding where E75 sits in the ICD-10-CM classification helps ensure proper coding:

Current CodeE75 — Disorders of sphingolipid metabolism and other lipid storage disorders
Sub-Codes 7 entries
E75.0GM2 gangliosidosisNon-BillableE75.00GM2 gangliosidosis, unspecifiedBillableE75.01Sandhoff diseaseBillableE75.02Tay-Sachs diseaseBillableE75.09Other GM2 gangliosidosisBillableE75.1Other and unspecified gangliosidosisNon-BillableE75.10Unspecified gangliosidosisBillableE75.11Mucolipidosis IVBillableE75.19Other gangliosidosisBillableE75.2Other sphingolipidosisNon-BillableE75.21Fabry (-Anderson) diseaseBillableE75.22Gaucher diseaseBillableE75.23Krabbe diseaseBillableE75.24Niemann-Pick diseaseNon-BillableE75.240Niemann-Pick disease type ABillableE75.241Niemann-Pick disease type BBillableE75.242Niemann-Pick disease type CBillableE75.243Niemann-Pick disease type DBillableE75.244Niemann-Pick disease type A/BBillableE75.248Other Niemann-Pick diseaseBillableE75.249Niemann-Pick disease, unspecifiedBillableE75.25Metachromatic leukodystrophyBillableE75.26Sulfatase deficiencyBillableE75.27Pelizaeus-Merzbacher diseaseBillableE75.28Canavan diseaseBillableE75.29Other sphingolipidosisBillableE75.3Sphingolipidosis, unspecifiedBillableE75.4Neuronal ceroid lipofuscinosisBillableE75.5Other lipid storage disordersBillableE75.6Lipid storage disorder, unspecifiedBillable
Related Codes

Frequently Asked Questions

Is E75 a billable ICD-10-CM code?

No, E75 is a non-billable/non-specific code. You should use a more specific sub-code for billing and reimbursement.

What does E75 mean?

E75 is the ICD-10-CM diagnosis code for "Disorders of sphingolipid metabolism and other lipid storage disorders". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What section is E75 in?

E75 is located in Section E70-E88 — "Metabolic disorders" within Chapter 4 of the ICD-10-CM Tabular List.

What are the sub-codes of E75?

E75 has 7 sub-code(s) that provide more specific detail: E75.0, E75.1, E75.2, E75.3, E75.4 and more.

When should I use E75?

Use E75 when the patients documented diagnosis matches "Disorders of sphingolipid metabolism and other lipid storage disorders" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Disorders of sphingolipid metabolism and other lipid storage disorders?

The ICD-10-CM code for Disorders of sphingolipid metabolism and other lipid storage disorders is E75.

Can E75 be used for primary diagnosis?

No, E75 is non-billable. Use a more specific sub-code for primary diagnosis billing.

What chapter is E75 in?

E75 is in Chapter 4 of the ICD-10-CM Tabular List.

What conditions are excluded from E75?

Type 1 Excludes for E75 include: mucolipidosis, types I-III (E77.0-E77.1); Refsum's disease (G60.1).

Is E75 valid for 2026?

Yes, E75 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousE74.9Disorder of carbohydrate metabolism, unspecifiedNext →E75.0GM2 gangliosidosis
Code Details
E75
Disorders of sphingolipid metabolism and other lipid storage disorders
Non-Billable / Non-Specific Code
4 — Endocrine, nutritional and metabolic diseases (E00-E89)
E70-E88 — Metabolic disorders
2026 ICD-10-CM