G71.035
Billable

Limb girdle muscular dystrophy due to anoctamin-5 dysfunction

Billable / Specific Code

What is Limb girdle muscular dystrophy due to anoctamin-5 dysfunction?

ICD-10-CM G71.035 is the diagnosis code for Limb girdle muscular dystrophy due to anoctamin-5 dysfunction. This code falls under the section "Diseases of myoneural junction and muscle" within Chapter 6 — Diseases of the nervous system (G00-G99). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

💡 Inclusions

Coding Guidelines for G71.035

✅ This Code Includes

  • Anoctamin-5-related LGMD R12
  • Anoctaminopathy
  • Autosomal recessive limb girdle muscular dystrophy type 2L
  • Miyoshi myopathy type 3

ICD-10-CM Code Hierarchy

Understanding where G71.035 sits in the ICD-10-CM classification helps ensure proper coding:

Current CodeG71.035 — Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
Sub-Codes (1918)
A00A01A02A03A04A05A06A07A08A09A15A17A18A19A20A21A22A23A24A25A26A27A28A30A31A32A33A34A35A36A37A38A39A40A41A42A43A44A46A48A49A50A51A52A53A54A55A56A57A58A59A60A63A64A65A66A67A68A69A70A71A74A75A77A78A79A80A81A82A83A84A85A86A87A88A89A90A91A92A93A94A95A96A98A99B00B01B02B03B04B05B06B07B08B09B10B15B16B17B18B19B20B25B26B27B30B33B34B35B36B37B38B39B40B41B42B43B44B45B46B47B48B49B50B51B52B53B54B55B56B57B58B59B60B64B65B66B67B68B69B70B71B72B73B74B75B76B77B78B79B80B81B82B83B85B86B87B88B89B90B91B92B94B95B96B97B99C00C01C02C03C04C05C06C07C08C09C10C11C12C13C14C15C16C17C18C19C20C21C22C23C24C25C26C30C31C32C33C34C37C38C39C40C41C43C44C45C46C47C48C49C4AC50C51C52C53C54C55C56C57C58C60C61C62C63C64C65C66C67C68C69C70C71C72C73C74C75C76C77C78C79C7AC7BC80C81C82C83C84C85C86C88C90C91C92C93C94C95C96D00D01D02D03D04D05D06D07D09D10D11D12D13D14D15D16D17D18D19D20D21D22D23D24D25D26D27D28D29D30D31D32D33D34D35D36D37D38D39D3AD40D41D42D43D44D45D46D47D48D49D50D51D52D53D55D56D57D58D59D60D61D62D63D64D65D66D67D68D69D70D71D72D73D74D75D76D77D78D80D81D82D83D84D86D89E00E01E02E03E04E05E06E07E08E09E10E11E13E15E16E20E21E22E23E24E25E26E27E28E29E30E31E32E34E35E36E40E41E42E43E44E45E46E50E51E52E53E54E55E56E58E59E60E61E63E64E65E66E67E68E70E71E72E73E74E75E76E77E78E79E80E83E84E85E86E87E88E89F01F02F03F04F05F06F07F09F10F11F12F13F14F15F16F17F18F19F20F21F22F23F24F25F28F29F30F31F32F33F34F39F40F41F42F43F44F45F48F50F51F52F53F54F55F59F60F63F64F65F66F68F69F70F71F72F73F78F79F80F81F82F84F88F89F90F91F93F94F95F98F99G00G01G02G03G04G05G06G07G08G09G10G11G12G13G14G20G21G23G24G25G26G30G31G32G35G36G37G40G43G44G45G46G47G50G51G52G53G54G55G56G57G58G59G60G61G62G63G64G65G70G71G72G73G80G81G82G83G89G90G91G92G93G94G95G96G97G98G99H00H01H02H04H05H10H11H15H16H17H18H20H21H22H25H26H27H28H30H31H32H33H34H35H36H40H42H43H44H46H47H49H50H51H52H53H54H55H57H59H60H61H62H65H66H67H68H69H70H71H72H73H74H75H80H81H82H83H90H91H92H93H94H95I00I01I02I05I06I07I08I09I10I11I12I13I15I16I1AI20I21I22I23I24I25I26I27I28I30I31I32I33I34I35I36I37I38I39I40I41I42I43I44I45I46I47I48I49I50I51I52I5AI60I61I62I63I65I66I67I68I69I70I71I72I73I74I75I76I77I78I79I80I81I82I83I85I86I87I88I89I95I96I97I99J00J01J02J03J04J05J06J09J10J11J12J13J14J15J16J17J18J20J21J22J30J31J32J33J34J35J36J37J38J39J40J41J42J43J44J45J47J4AJ60J61J62J63J64J65J66J67J68J69J70J80J81J82J84J85J86J90J91J92J93J94J95J96J98J99K00K01K02K03K04K05K06K08K09K11K12K13K14K20K21K22K23K25K26K27K28K29K30K31K35K36K37K38K40K41K42K43K44K45K46K50K51K52K55K56K57K58K59K60K61K62K63K64K65K66K67K68K70K71K72K73K74K75K76K77K80K81K82K83K85K86K87K90K91K92K94K95L00L01L02L03L04L05L08L10L11L12L13L14L20L21L22L23L24L25L26L27L28L29L30L40L41L42L43L44L45L49L50L51L52L53L54L55L56L57L58L59L60L62L63L64L65L66L67L68L70L71L72L73L74L75L76L80L81L82L83L84L85L86L87L88L89L90L91L92L93L94L95L97L98L99M00M01M02M04M05M06M07M08M10M11M12M13M14M15M16M17M18M19M1AM20M21M22M23M24M25M26M27M30M31M32M33M34M35M36M40M41M42M43M45M46M47M48M49M50M51M53M54M60M61M62M63M65M66M67M70M71M72M75M76M77M79M80M81M83M84M85M86M87M88M89M90M91M92M93M94M95M96M97M99N00N01N02N03N04N05N06N07N08N10N11N12N13N14N15N16N17N18N19N20N21N22N23N25N26N27N28N29N30N31N32N33N34N35N36N37N39N40N41N42N43N44N45N46N47N48N49N50N51N52N53N60N61N62N63N64N65N70N71N72N73N74N75N76N77N80N81N82N83N84N85N86N87N88N89N90N91N92N93N94N95N96N97N98N99O00O01O02O03O04O07O08O09O10O11O12O13O14O15O16O20O21O22O23O24O25O26O28O29O30O31O32O33O34O35O36O40O41O42O43O44O45O46O47O48O60O61O62O63O64O65O66O67O68O69O70O71O72O73O74O75O76O77O80O82O85O86O87O88O89O90O91O92O94O98O99O9AP00P01P02P03P04P05P07P08P09P10P11P12P13P14P15P19P22P23P24P25P26P27P28P29P35P36P37P38P39P50P51P52P53P54P55P56P57P58P59P60P61P70P71P72P74P76P77P78P80P81P83P84P90P91P92P93P94P95P96Q00Q01Q02Q03Q04Q05Q06Q07Q10Q11Q12Q13Q14Q15Q16Q17Q18Q20Q21Q22Q23Q24Q25Q26Q27Q28Q30Q31Q32Q33Q34Q35Q36Q37Q38Q39Q40Q41Q42Q43Q44Q45Q50Q51Q52Q53Q54Q55Q56Q60Q61Q62Q63Q64Q65Q66Q67Q68Q69Q70Q71Q72Q73Q74Q75Q76Q77Q78Q79Q80Q81Q82Q83Q84Q85Q86Q87Q89Q90Q91Q92Q93Q95Q96Q97Q98Q99QA0R00R01R03R04R05R06R07R09R10R11R12R13R14R15R16R17R18R19R20R21R22R23R25R26R27R29R30R31R32R33R34R35R36R37R39R40R41R42R43R44R45R46R47R48R49R50R51R52R53R54R55R56R57R58R59R60R61R62R63R64R65R68R69R70R71R73R74R75R76R77R78R79R80R81R82R83R84R85R86R87R88R89R90R91R92R93R94R97R99S00S01S02S03S04S05S06S07S08S09S10S11S12S13S14S15S16S17S19S20S21S22S23S24S25S26S27S28S29S30S31S32S33S34S35S36S37S38S39S40S41S42S43S44S45S46S47S48S49S50S51S52S53S54S55S56S57S58S59S60S61S62S63S64S65S66S67S68S69S70S71S72S73S74S75S76S77S78S79S80S81S82S83S84S85S86S87S88S89S90S91S92S93S94S95S96S97S98S99T07T14T15T16T17T18T19T20T21T22T23T24T25T26T27T28T30T31T32T33T34T36T37T38T39T40T41T42T43T44T45T46T47T48T49T50T51T52T53T54T55T56T57T58T59T60T61T62T63T64T65T66T67T68T69T70T71T73T74T75T76T78T79T80T81T82T83T84T85T86T87T88U07U09V00V01V02V03V04V05V06V09V10V11V12V13V14V15V16V17V18V19V20V21V22V23V24V25V26V27V28V29V30V31V32V33V34V35V36V37V38V39V40V41V42V43V44V45V46V47V48V49V50V51V52V53V54V55V56V57V58V59V60V61V62V63V64V65V66V67V68V69V70V71V72V73V74V75V76V77V78V79V80V81V82V83V84V85V86V87V88V89V90V91V92V93V94V95V96V97V98V99W00W01W03W04W05W06W07W08W09W10W11W12W13W1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Related Codes

Frequently Asked Questions

Is G71.035 a billable ICD-10-CM code?

Yes, G71.035 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What does G71.035 mean?

G71.035 is the ICD-10-CM diagnosis code for "Limb girdle muscular dystrophy due to anoctamin-5 dysfunction". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of G71.035?

The parent code of G71.035 is G71.03 ("Limb girdle muscular dystrophies"). G71.035 provides a more specific classification within this category.

What section is G71.035 in?

G71.035 is located in Section G70-G73 — "Diseases of myoneural junction and muscle" within Chapter 6 of the ICD-10-CM Tabular List.

What are the sub-codes of G71.035?

G71.035 has 1918 sub-code(s) that provide more specific detail: A00, A01, A02, A03, A04 and more.

When should I use G71.035?

Use G71.035 when the patients documented diagnosis matches "Limb girdle muscular dystrophy due to anoctamin-5 dysfunction" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Limb girdle muscular dystrophy due to anoctamin-5 dysfunction?

The ICD-10-CM code for Limb girdle muscular dystrophy due to anoctamin-5 dysfunction is G71.035.

Can G71.035 be used for primary diagnosis?

Yes, G71.035 can be used as a primary diagnosis code since it is billable and specific.

What chapter is G71.035 in?

G71.035 is in Chapter 6 of the ICD-10-CM Tabular List.

Is G71.035 valid for 2026?

Yes, G71.035 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousG71.0349Limb girdle muscular dystrophy due to other sarcoglycan dysfunctionNext →G71.036Limb girdle muscular dystrophy due to fukutin related protein dysfunction
Code Details
G71.035
Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
Billable / Specific Code
6 — Diseases of the nervous system (G00-G99)
G70-G73 — Diseases of myoneural junction and muscle
2026 ICD-10-CM