L81.3
Billable

Café au lait spots

Billable / Specific Code

What is Café au lait spots?

ICD-10-CM L81.3 is the diagnosis code for Café au lait spots. This code falls under the section "Other disorders of the skin and subcutaneous tissue" within Chapter 12 — Diseases of the skin and subcutaneous tissue (L00-L99). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

Coding Guidelines for L81.3

Always refer to the official ICD-10-CM Tabular List for complete coding guidelines. Ensure documentation supports the specificity of the code selected. When in doubt, consult a certified medical coder or the latest CMS guidelines.

ICD-10-CM Code Hierarchy

Understanding where L81.3 sits in the ICD-10-CM classification helps ensure proper coding:

Current CodeL81.3 — Café au lait spots
Sub-Codes (1918)
A00A01A02A03A04A05A06A07A08A09A15A17A18A19A20A21A22A23A24A25A26A27A28A30A31A32A33A34A35A36A37A38A39A40A41A42A43A44A46A48A49A50A51A52A53A54A55A56A57A58A59A60A63A64A65A66A67A68A69A70A71A74A75A77A78A79A80A81A82A83A84A85A86A87A88A89A90A91A92A93A94A95A96A98A99B00B01B02B03B04B05B06B07B08B09B10B15B16B17B18B19B20B25B26B27B30B33B34B35B36B37B38B39B40B41B42B43B44B45B46B47B48B49B50B51B52B53B54B55B56B57B58B59B60B64B65B66B67B68B69B70B71B72B73B74B75B76B77B78B79B80B81B82B83B85B86B87B88B89B90B91B92B94B95B96B97B99C00C01C02C03C04C05C06C07C08C09C10C11C12C13C14C15C16C17C18C19C20C21C22C23C24C25C26C30C31C32C33C34C37C38C39C40C41C43C44C45C46C47C48C49C4AC50C51C52C53C54C55C56C57C58C60C61C62C63C64C65C66C67C68C69C70C71C72C73C74C75C76C77C78C79C7AC7BC80C81C82C83C84C85C86C88C90C91C92C93C94C95C96D00D01D02D03D04D05D06D07D09D10D11D12D13D14D15D16D17D18D19D20D21D22D23D24D25D26D27D28D29D30D31D32D33D34D35D36D37D38D39D3AD40D41D42D43D44D45D46D47D48D49D50D51D52D53D55D56D57D58D59D60D61D62D63D64D65D66D67D68D69D70D71D72D73D74D75D76D77D78D80D81D82D83D84D86D89E00E01E02E03E04E05E06E07E08E09E10E11E13E15E16E20E21E22E23E24E25E26E27E28E29E30E31E32E34E35E36E40E41E42E43E44E45E46E50E51E52E53E54E55E56E58E59E60E61E63E64E65E66E67E68E70E71E72E73E74E75E76E77E78E79E80E83E84E85E86E87E88E89F01F02F03F04F05F06F07F09F10F11F12F13F14F15F16F17F18F19F20F21F22F23F24F25F28F29F30F31F32F33F34F39F40F41F42F43F44F45F48F50F51F52F53F54F55F59F60F63F64F65F66F68F69F70F71F72F73F78F79F80F81F82F84F88F89F90F91F93F94F95F98F99G00G01G02G03G04G05G06G07G08G09G10G11G12G13G14G20G21G23G24G25G26G30G31G32G35G36G37G40G43G44G45G46G47G50G51G52G53G54G55G56G57G58G59G60G61G62G63G64G65G70G71G72G73G80G81G82G83G89G90G91G92G93G94G95G96G97G98G99H00H01H02H04H05H10H11H15H16H17H18H20H21H22H25H26H27H28H30H31H32H33H34H35H36H40H42H43H44H46H47H49H50H51H52H53H54H55H57H59H60H61H62H65H66H67H68H69H70H71H72H73H74H75H80H81H82H83H90H91H92H93H94H95I00I01I02I05I06I07I08I09I10I11I12I13I15I16I1AI20I21I22I23I24I25I26I27I28I30I31I32I33I34I35I36I37I38I39I40I41I42I43I44I45I46I47I48I49I50I51I52I5AI60I61I62I63I65I66I67I68I69I70I71I72I73I74I75I76I77I78I79I80I81I82I83I85I86I87I88I89I95I96I97I99J00J01J02J03J04J05J06J09J10J11J12J13J14J15J16J17J18J20J21J22J30J31J32J33J34J35J36J37J38J39J40J41J42J43J44J45J47J4AJ60J61J62J63J64J65J66J67J68J69J70J80J81J82J84J85J86J90J91J92J93J94J95J96J98J99K00K01K02K03K04K05K06K08K09K11K12K13K14K20K21K22K23K25K26K27K28K29K30K31K35K36K37K38K40K41K42K43K44K45K46K50K51K52K55K56K57K58K59K60K61K62K63K64K65K66K67K68K70K71K72K73K74K75K76K77K80K81K82K83K85K86K87K90K91K92K94K95L00L01L02L03L04L05L08L10L11L12L13L14L20L21L22L23L24L25L26L27L28L29L30L40L41L42L43L44L45L49L50L51L52L53L54L55L56L57L58L59L60L62L63L64L65L66L67L68L70L71L72L73L74L75L76L80L81L82L83L84L85L86L87L88L89L90L91L92L93L94L95L97L98L99M00M01M02M04M05M06M07M08M10M11M12M13M14M15M16M17M18M19M1AM20M21M22M23M24M25M26M27M30M31M32M33M34M35M36M40M41M42M43M45M46M47M48M49M50M51M53M54M60M61M62M63M65M66M67M70M71M72M75M76M77M79M80M81M83M84M85M86M87M88M89M90M91M92M93M94M95M96M97M99N00N01N02N03N04N05N06N07N08N10N11N12N13N14N15N16N17N18N19N20N21N22N23N25N26N27N28N29N30N31N32N33N34N35N36N37N39N40N41N42N43N44N45N46N47N48N49N50N51N52N53N60N61N62N63N64N65N70N71N72N73N74N75N76N77N80N81N82N83N84N85N86N87N88N89N90N91N92N93N94N95N96N97N98N99O00O01O02O03O04O07O08O09O10O11O12O13O14O15O16O20O21O22O23O24O25O26O28O29O30O31O32O33O34O35O36O40O41O42O43O44O45O46O47O48O60O61O62O63O64O65O66O67O68O69O70O71O72O73O74O75O76O77O80O82O85O86O87O88O89O90O91O92O94O98O99O9AP00P01P02P03P04P05P07P08P09P10P11P12P13P14P15P19P22P23P24P25P26P27P28P29P35P36P37P38P39P50P51P52P53P54P55P56P57P58P59P60P61P70P71P72P74P76P77P78P80P81P83P84P90P91P92P93P94P95P96Q00Q01Q02Q03Q04Q05Q06Q07Q10Q11Q12Q13Q14Q15Q16Q17Q18Q20Q21Q22Q23Q24Q25Q26Q27Q28Q30Q31Q32Q33Q34Q35Q36Q37Q38Q39Q40Q41Q42Q43Q44Q45Q50Q51Q52Q53Q54Q55Q56Q60Q61Q62Q63Q64Q65Q66Q67Q68Q69Q70Q71Q72Q73Q74Q75Q76Q77Q78Q79Q80Q81Q82Q83Q84Q85Q86Q87Q89Q90Q91Q92Q93Q95Q96Q97Q98Q99QA0R00R01R03R04R05R06R07R09R10R11R12R13R14R15R16R17R18R19R20R21R22R23R25R26R27R29R30R31R32R33R34R35R36R37R39R40R41R42R43R44R45R46R47R48R49R50R51R52R53R54R55R56R57R58R59R60R61R62R63R64R65R68R69R70R71R73R74R75R76R77R78R79R80R81R82R83R84R85R86R87R88R89R90R91R92R93R94R97R99S00S01S02S03S04S05S06S07S08S09S10S11S12S13S14S15S16S17S19S20S21S22S23S24S25S26S27S28S29S30S31S32S33S34S35S36S37S38S39S40S41S42S43S44S45S46S47S48S49S50S51S52S53S54S55S56S57S58S59S60S61S62S63S64S65S66S67S68S69S70S71S72S73S74S75S76S77S78S79S80S81S82S83S84S85S86S87S88S89S90S91S92S93S94S95S96S97S98S99T07T14T15T16T17T18T19T20T21T22T23T24T25T26T27T28T30T31T32T33T34T36T37T38T39T40T41T42T43T44T45T46T47T48T49T50T51T52T53T54T55T56T57T58T59T60T61T62T63T64T65T66T67T68T69T70T71T73T74T75T76T78T79T80T81T82T83T84T85T86T87T88U07U09V00V01V02V03V04V05V06V09V10V11V12V13V14V15V16V17V18V19V20V21V22V23V24V25V26V27V28V29V30V31V32V33V34V35V36V37V38V39V40V41V42V43V44V45V46V47V48V49V50V51V52V53V54V55V56V57V58V59V60V61V62V63V64V65V66V67V68V69V70V71V72V73V74V75V76V77V78V79V80V81V82V83V84V85V86V87V88V89V90V91V92V93V94V95V96V97V98V99W00W01W03W04W05W06W07W08W09W10W11W12W13W1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Related Codes

Frequently Asked Questions

Is L81.3 a billable ICD-10-CM code?

Yes, L81.3 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What does L81.3 mean?

L81.3 is the ICD-10-CM diagnosis code for "Café au lait spots". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of L81.3?

The parent code of L81.3 is L81 ("Other disorders of pigmentation"). L81.3 provides a more specific classification within this category.

What section is L81.3 in?

L81.3 is located in Section L80-L99 — "Other disorders of the skin and subcutaneous tissue" within Chapter 12 of the ICD-10-CM Tabular List.

What are the sub-codes of L81.3?

L81.3 has 1918 sub-code(s) that provide more specific detail: A00, A01, A02, A03, A04 and more.

When should I use L81.3?

Use L81.3 when the patients documented diagnosis matches "Café au lait spots" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Café au lait spots?

The ICD-10-CM code for Café au lait spots is L81.3.

Can L81.3 be used for primary diagnosis?

Yes, L81.3 can be used as a primary diagnosis code since it is billable and specific.

What chapter is L81.3 in?

L81.3 is in Chapter 12 of the ICD-10-CM Tabular List.

Is L81.3 valid for 2026?

Yes, L81.3 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousL81.2FrecklesNext →L81.4Other melanin hyperpigmentation
Code Details
L81.3
Café au lait spots
Billable / Specific Code
12 — Diseases of the skin and subcutaneous tissue (L00-L99)
L80-L99 — Other disorders of the skin and subcutaneous tissue
2026 ICD-10-CM