Q25.4
Non-Billable

Other congenital malformations of aorta

Non-Billable / Non-Specific Code

What is Other congenital malformations of aorta?

ICD-10-CM Q25.4 is the diagnosis code for Other congenital malformations of aorta. This code falls under the section "Congenital malformations of the circulatory system" within Chapter 17 — Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0). It is a non-billable/non-specific ICD-10-CM code that should not be used for reimbursement. A more specific sub-code is required for billing. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

⛔ Excludes1

Coding Guidelines for Q25.4

⛔ Type 1 Excludes (Never code together)

The following conditions should never be coded at the same time as Q25.4. They are mutually exclusive:

  • hypoplasia of aorta in hypoplastic left heart syndrome (Q23.4)

ICD-10-CM Code Hierarchy

Understanding where Q25.4 sits in the ICD-10-CM classification helps ensure proper coding:

Current CodeQ25.4 — Other congenital malformations of aorta
Sub-Codes (1918)
A00A01A02A03A04A05A06A07A08A09A15A17A18A19A20A21A22A23A24A25A26A27A28A30A31A32A33A34A35A36A37A38A39A40A41A42A43A44A46A48A49A50A51A52A53A54A55A56A57A58A59A60A63A64A65A66A67A68A69A70A71A74A75A77A78A79A80A81A82A83A84A85A86A87A88A89A90A91A92A93A94A95A96A98A99B00B01B02B03B04B05B06B07B08B09B10B15B16B17B18B19B20B25B26B27B30B33B34B35B36B37B38B39B40B41B42B43B44B45B46B47B48B49B50B51B52B53B54B55B56B57B58B59B60B64B65B66B67B68B69B70B71B72B73B74B75B76B77B78B79B80B81B82B83B85B86B87B88B89B90B91B92B94B95B96B97B99C00C01C02C03C04C05C06C07C08C09C10C11C12C13C14C15C16C17C18C19C20C21C22C23C24C25C26C30C31C32C33C34C37C38C39C40C41C43C44C45C46C47C48C49C4AC50C51C52C53C54C55C56C57C58C60C61C62C63C64C65C66C67C68C69C70C71C72C73C74C75C76C77C78C79C7AC7BC80C81C82C83C84C85C86C88C90C91C92C93C94C95C96D00D01D02D03D04D05D06D07D09D10D11D12D13D14D15D16D17D18D19D20D21D22D23D24D25D26D27D28D29D30D31D32D33D34D35D36D37D38D39D3AD40D41D42D43D44D45D46D47D48D49D50D51D52D53D55D56D57D58D59D60D61D62D63D64D65D66D67D68D69D70D71D72D73D74D75D76D77D78D80D81D82D83D84D86D89E00E01E02E03E04E05E06E07E08E09E10E11E13E15E16E20E21E22E23E24E25E26E27E28E29E30E31E32E34E35E36E40E41E42E43E44E45E46E50E51E52E53E54E55E56E58E59E60E61E63E64E65E66E67E68E70E71E72E73E74E75E76E77E78E79E80E83E84E85E86E87E88E89F01F02F03F04F05F06F07F09F10F11F12F13F14F15F16F17F18F19F20F21F22F23F24F25F28F29F30F31F32F33F34F39F40F41F42F43F44F45F48F50F51F52F53F54F55F59F60F63F64F65F66F68F69F70F71F72F73F78F79F80F81F82F84F88F89F90F91F93F94F95F98F99G00G01G02G03G04G05G06G07G08G09G10G11G12G13G14G20G21G23G24G25G26G30G31G32G35G36G37G40G43G44G45G46G47G50G51G52G53G54G55G56G57G58G59G60G61G62G63G64G65G70G71G72G73G80G81G82G83G89G90G91G92G93G94G95G96G97G98G99H00H01H02H04H05H10H11H15H16H17H18H20H21H22H25H26H27H28H30H31H32H33H34H35H36H40H42H43H44H46H47H49H50H51H52H53H54H55H57H59H60H61H62H65H66H67H68H69H70H71H72H73H74H75H80H81H82H83H90H91H92H93H94H95I00I01I02I05I06I07I08I09I10I11I12I13I15I16I1AI20I21I22I23I24I25I26I27I28I30I31I32I33I34I35I36I37I38I39I40I41I42I43I44I45I46I47I48I49I50I51I52I5AI60I61I62I63I65I66I67I68I69I70I71I72I73I74I75I76I77I78I79I80I81I82I83I85I86I87I88I89I95I96I97I99J00J01J02J03J04J05J06J09J10J11J12J13J14J15J16J17J18J20J21J22J30J31J32J33J34J35J36J37J38J39J40J41J42J43J44J45J47J4AJ60J61J62J63J64J65J66J67J68J69J70J80J81J82J84J85J86J90J91J92J93J94J95J96J98J99K00K01K02K03K04K05K06K08K09K11K12K13K14K20K21K22K23K25K26K27K28K29K30K31K35K36K37K38K40K41K42K43K44K45K46K50K51K52K55K56K57K58K59K60K61K62K63K64K65K66K67K68K70K71K72K73K74K75K76K77K80K81K82K83K85K86K87K90K91K92K94K95L00L01L02L03L04L05L08L10L11L12L13L14L20L21L22L23L24L25L26L27L28L29L30L40L41L42L43L44L45L49L50L51L52L53L54L55L56L57L58L59L60L62L63L64L65L66L67L68L70L71L72L73L74L75L76L80L81L82L83L84L85L86L87L88L89L90L91L92L93L94L95L97L98L99M00M01M02M04M05M06M07M08M10M11M12M13M14M15M16M17M18M19M1AM20M21M22M23M24M25M26M27M30M31M32M33M34M35M36M40M41M42M43M45M46M47M48M49M50M51M53M54M60M61M62M63M65M66M67M70M71M72M75M76M77M79M80M81M83M84M85M86M87M88M89M90M91M92M93M94M95M96M97M99N00N01N02N03N04N05N06N07N08N10N11N12N13N14N15N16N17N18N19N20N21N22N23N25N26N27N28N29N30N31N32N33N34N35N36N37N39N40N41N42N43N44N45N46N47N48N49N50N51N52N53N60N61N62N63N64N65N70N71N72N73N74N75N76N77N80N81N82N83N84N85N86N87N88N89N90N91N92N93N94N95N96N97N98N99O00O01O02O03O04O07O08O09O10O11O12O13O14O15O16O20O21O22O23O24O25O26O28O29O30O31O32O33O34O35O36O40O41O42O43O44O45O46O47O48O60O61O62O63O64O65O66O67O68O69O70O71O72O73O74O75O76O77O80O82O85O86O87O88O89O90O91O92O94O98O99O9AP00P01P02P03P04P05P07P08P09P10P11P12P13P14P15P19P22P23P24P25P26P27P28P29P35P36P37P38P39P50P51P52P53P54P55P56P57P58P59P60P61P70P71P72P74P76P77P78P80P81P83P84P90P91P92P93P94P95P96Q00Q01Q02Q03Q04Q05Q06Q07Q10Q11Q12Q13Q14Q15Q16Q17Q18Q20Q21Q22Q23Q24Q25Q26Q27Q28Q30Q31Q32Q33Q34Q35Q36Q37Q38Q39Q40Q41Q42Q43Q44Q45Q50Q51Q52Q53Q54Q55Q56Q60Q61Q62Q63Q64Q65Q66Q67Q68Q69Q70Q71Q72Q73Q74Q75Q76Q77Q78Q79Q80Q81Q82Q83Q84Q85Q86Q87Q89Q90Q91Q92Q93Q95Q96Q97Q98Q99QA0R00R01R03R04R05R06R07R09R10R11R12R13R14R15R16R17R18R19R20R21R22R23R25R26R27R29R30R31R32R33R34R35R36R37R39R40R41R42R43R44R45R46R47R48R49R50R51R52R53R54R55R56R57R58R59R60R61R62R63R64R65R68R69R70R71R73R74R75R76R77R78R79R80R81R82R83R84R85R86R87R88R89R90R91R92R93R94R97R99S00S01S02S03S04S05S06S07S08S09S10S11S12S13S14S15S16S17S19S20S21S22S23S24S25S26S27S28S29S30S31S32S33S34S35S36S37S38S39S40S41S42S43S44S45S46S47S48S49S50S51S52S53S54S55S56S57S58S59S60S61S62S63S64S65S66S67S68S69S70S71S72S73S74S75S76S77S78S79S80S81S82S83S84S85S86S87S88S89S90S91S92S93S94S95S96S97S98S99T07T14T15T16T17T18T19T20T21T22T23T24T25T26T27T28T30T31T32T33T34T36T37T38T39T40T41T42T43T44T45T46T47T48T49T50T51T52T53T54T55T56T57T58T59T60T61T62T63T64T65T66T67T68T69T70T71T73T74T75T76T78T79T80T81T82T83T84T85T86T87T88U07U09V00V01V02V03V04V05V06V09V10V11V12V13V14V15V16V17V18V19V20V21V22V23V24V25V26V27V28V29V30V31V32V33V34V35V36V37V38V39V40V41V42V43V44V45V46V47V48V49V50V51V52V53V54V55V56V57V58V59V60V61V62V63V64V65V66V67V68V69V70V71V72V73V74V75V76V77V78V79V80V81V82V83V84V85V86V87V88V89V90V91V92V93V94V95V96V97V98V99W00W01W03W04W05W06W07W08W09W10W11W12W13W14W15W16W17W18W19W20W21W22W23W24W25W26W27W28W29W30W31W32W33W34W35W36W37W38W39W40W42W44W45W46W49W50W51W52W53W54W55W56W57W58W59W60W61W62W64W65W67W69W73W74W85W86W88W89W90W92W93W94W99X00X01X02X03X04X05X06X08X10X11X12X13X14X15X16X17X18X19X30X31X32X34X35X36X37X38X39X50X52X58X71X72X73X74X75X76X77X78X79X80X81X82X83X92X93X94X95X96X97X98X99Y00Y01Y02Y03Y04Y07Y08Y09Y21Y22Y23Y24Y25Y26Y27Y28Y29Y30Y31Y32Y33Y35Y36Y37Y38Y62Y63Y64Y65Y66Y69Y70Y71Y72Y73Y74Y75Y76Y77Y78Y79Y80Y81Y82Y83Y84Y90Y92Y93Y95Y99Z00Z01Z02Z03Z04Z05Z08Z09Z11Z12Z13Z14Z15Z16Z17Z18Z19Z20Z21Z22Z23Z28Z29Z30Z31Z32Z33Z34Z36Z37Z38Z39Z3AZ40Z41Z42Z43Z44Z45Z46Z47Z48Z49Z51Z52Z53Z55Z56Z57Z58Z59Z60Z62Z63Z64Z65Z66Z67Z68Z69Z70Z71Z72Z73Z74Z75Z76Z77Z78Z79Z80Z81Z82Z83Z84Z85Z86Z87Z88Z89Z90Z91Z92Z93Z94Z95Z96Z97Z98Z99
Sub-Codes 10 entries
Q25.40Congenital malformation of aorta unspecifiedBillableQ25.41Absence and aplasia of aortaBillableQ25.42Hypoplasia of aortaBillableQ25.43Congenital aneurysm of aortaBillableQ25.44Congenital dilation of aortaBillableQ25.45Double aortic archBillableQ25.46Tortuous aortic archBillableQ25.47Right aortic archBillableQ25.48Anomalous origin of subclavian arteryBillableQ25.49Other congenital malformations of aortaBillable
Related Codes

Frequently Asked Questions

Is Q25.4 a billable ICD-10-CM code?

No, Q25.4 is a non-billable/non-specific code. You should use a more specific sub-code for billing and reimbursement.

What does Q25.4 mean?

Q25.4 is the ICD-10-CM diagnosis code for "Other congenital malformations of aorta". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of Q25.4?

The parent code of Q25.4 is Q25 ("Congenital malformations of great arteries"). Q25.4 provides a more specific classification within this category.

What section is Q25.4 in?

Q25.4 is located in Section Q20-Q28 — "Congenital malformations of the circulatory system" within Chapter 17 of the ICD-10-CM Tabular List.

What are the sub-codes of Q25.4?

Q25.4 has 1918 sub-code(s) that provide more specific detail: A00, A01, A02, A03, A04 and more.

When should I use Q25.4?

Use Q25.4 when the patients documented diagnosis matches "Other congenital malformations of aorta" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Other congenital malformations of aorta?

The ICD-10-CM code for Other congenital malformations of aorta is Q25.4.

Can Q25.4 be used for primary diagnosis?

No, Q25.4 is non-billable. Use a more specific sub-code for primary diagnosis billing.

What chapter is Q25.4 in?

Q25.4 is in Chapter 17 of the ICD-10-CM Tabular List.

What conditions are excluded from Q25.4?

Type 1 Excludes for Q25.4 include: hypoplasia of aorta in hypoplastic left heart syndrome (Q23.4).

Is Q25.4 valid for 2026?

Yes, Q25.4 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousQ25.3Supravalvular aortic stenosisNext →Q25.40Congenital malformation of aorta unspecified
Code Details
Q25.4
Other congenital malformations of aorta
Non-Billable / Non-Specific Code
17 — Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
Q20-Q28 — Congenital malformations of the circulatory system
2026 ICD-10-CM