M34.1
Billable

CR(E)ST syndrome

Billable / Specific Code

What is CR(E)ST syndrome?

ICD-10-CM M34.1 is the diagnosis code for CR(E)ST syndrome. This code falls under the section "Systemic connective tissue disorders" within Chapter 13 — Diseases of the musculoskeletal system and connective tissue (M00-M99). It is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

💡 Inclusions

Coding Guidelines for M34.1

✅ This Code Includes

  • Combination of calcinosis, Raynaud's phenomenon, esophageal dysfunction, sclerodactyly, telangiectasia

ICD-10-CM Code Hierarchy

Understanding where M34.1 sits in the ICD-10-CM classification helps ensure proper coding:

Current CodeM34.1 — CR(E)ST syndrome
Sub-Codes (1918)
A00A01A02A03A04A05A06A07A08A09A15A17A18A19A20A21A22A23A24A25A26A27A28A30A31A32A33A34A35A36A37A38A39A40A41A42A43A44A46A48A49A50A51A52A53A54A55A56A57A58A59A60A63A64A65A66A67A68A69A70A71A74A75A77A78A79A80A81A82A83A84A85A86A87A88A89A90A91A92A93A94A95A96A98A99B00B01B02B03B04B05B06B07B08B09B10B15B16B17B18B19B20B25B26B27B30B33B34B35B36B37B38B39B40B41B42B43B44B45B46B47B48B49B50B51B52B53B54B55B56B57B58B59B60B64B65B66B67B68B69B70B71B72B73B74B75B76B77B78B79B80B81B82B83B85B86B87B88B89B90B91B92B94B95B96B97B99C00C01C02C03C04C05C06C07C08C09C10C11C12C13C14C15C16C17C18C19C20C21C22C23C24C25C26C30C31C32C33C34C37C38C39C40C41C43C44C45C46C47C48C49C4AC50C51C52C53C54C55C56C57C58C60C61C62C63C64C65C66C67C68C69C70C71C72C73C74C75C76C77C78C79C7AC7BC80C81C82C83C84C85C86C88C90C91C92C93C94C95C96D00D01D02D03D04D05D06D07D09D10D11D12D13D14D15D16D17D18D19D20D21D22D23D24D25D26D27D28D29D30D31D32D33D34D35D36D37D38D39D3AD40D41D42D43D44D45D46D47D48D49D50D51D52D53D55D56D57D58D59D60D61D62D63D64D65D66D67D68D69D70D71D72D73D74D75D76D77D78D80D81D82D83D84D86D89E00E01E02E03E04E05E06E07E08E09E10E11E13E15E16E20E21E22E23E24E25E26E27E28E29E30E31E32E34E35E36E40E41E42E43E44E45E46E50E51E52E53E54E55E56E58E59E60E61E63E64E65E66E67E68E70E71E72E73E74E75E76E77E78E79E80E83E84E85E86E87E88E89F01F02F03F04F05F06F07F09F10F11F12F13F14F15F16F17F18F19F20F21F22F23F24F25F28F29F30F31F32F33F34F39F40F41F42F43F44F45F48F50F51F52F53F54F55F59F60F63F64F65F66F68F69F70F71F72F73F78F79F80F81F82F84F88F89F90F91F93F94F95F98F99G00G01G02G03G04G05G06G07G08G09G10G11G12G13G14G20G21G23G24G25G26G30G31G32G35G36G37G40G43G44G45G46G47G50G51G52G53G54G55G56G57G58G59G60G61G62G63G64G65G70G71G72G73G80G81G82G83G89G90G91G92G93G94G95G96G97G98G99H00H01H02H04H05H10H11H15H16H17H18H20H21H22H25H26H27H28H30H31H32H33H34H35H36H40H42H43H44H46H47H49H50H51H52H53H54H55H57H59H60H61H62H65H66H67H68H69H70H71H72H73H74H75H80H81H82H83H90H91H92H93H94H95I00I01I02I05I06I07I08I09I10I11I12I13I15I16I1AI20I21I22I23I24I25I26I27I28I30I31I32I33I34I35I36I37I38I39I40I41I42I43I44I45I46I47I48I49I50I51I52I5AI60I61I62I63I65I66I67I68I69I70I71I72I73I74I75I76I77I78I79I80I81I82I83I85I86I87I88I89I95I96I97I99J00J01J02J03J04J05J06J09J10J11J12J13J14J15J16J17J18J20J21J22J30J31J32J33J34J35J36J37J38J39J40J41J42J43J44J45J47J4AJ60J61J62J63J64J65J66J67J68J69J70J80J81J82J84J85J86J90J91J92J93J94J95J96J98J99K00K01K02K03K04K05K06K08K09K11K12K13K14K20K21K22K23K25K26K27K28K29K30K31K35K36K37K38K40K41K42K43K44K45K46K50K51K52K55K56K57K58K59K60K61K62K63K64K65K66K67K68K70K71K72K73K74K75K76K77K80K81K82K83K85K86K87K90K91K92K94K95L00L01L02L03L04L05L08L10L11L12L13L14L20L21L22L23L24L25L26L27L28L29L30L40L41L42L43L44L45L49L50L51L52L53L54L55L56L57L58L59L60L62L63L64L65L66L67L68L70L71L72L73L74L75L76L80L81L82L83L84L85L86L87L88L89L90L91L92L93L94L95L97L98L99M00M01M02M04M05M06M07M08M10M11M12M13M14M15M16M17M18M19M1AM20M21M22M23M24M25M26M27M30M31M32M33M34M35M36M40M41M42M43M45M46M47M48M49M50M51M53M54M60M61M62M63M65M66M67M70M71M72M75M76M77M79M80M81M83M84M85M86M87M88M89M90M91M92M93M94M95M96M97M99N00N01N02N03N04N05N06N07N08N10N11N12N13N14N15N16N17N18N19N20N21N22N23N25N26N27N28N29N30N31N32N33N34N35N36N37N39N40N41N42N43N44N45N46N47N48N49N50N51N52N53N60N61N62N63N64N65N70N71N72N73N74N75N76N77N80N81N82N83N84N85N86N87N88N89N90N91N92N93N94N95N96N97N98N99O00O01O02O03O04O07O08O09O10O11O12O13O14O15O16O20O21O22O23O24O25O26O28O29O30O31O32O33O34O35O36O40O41O42O43O44O45O46O47O48O60O61O62O63O64O65O66O67O68O69O70O71O72O73O74O75O76O77O80O82O85O86O87O88O89O90O91O92O94O98O99O9AP00P01P02P03P04P05P07P08P09P10P11P12P13P14P15P19P22P23P24P25P26P27P28P29P35P36P37P38P39P50P51P52P53P54P55P56P57P58P59P60P61P70P71P72P74P76P77P78P80P81P83P84P90P91P92P93P94P95P96Q00Q01Q02Q03Q04Q05Q06Q07Q10Q11Q12Q13Q14Q15Q16Q17Q18Q20Q21Q22Q23Q24Q25Q26Q27Q28Q30Q31Q32Q33Q34Q35Q36Q37Q38Q39Q40Q41Q42Q43Q44Q45Q50Q51Q52Q53Q54Q55Q56Q60Q61Q62Q63Q64Q65Q66Q67Q68Q69Q70Q71Q72Q73Q74Q75Q76Q77Q78Q79Q80Q81Q82Q83Q84Q85Q86Q87Q89Q90Q91Q92Q93Q95Q96Q97Q98Q99QA0R00R01R03R04R05R06R07R09R10R11R12R13R14R15R16R17R18R19R20R21R22R23R25R26R27R29R30R31R32R33R34R35R36R37R39R40R41R42R43R44R45R46R47R48R49R50R51R52R53R54R55R56R57R58R59R60R61R62R63R64R65R68R69R70R71R73R74R75R76R77R78R79R80R81R82R83R84R85R86R87R88R89R90R91R92R93R94R97R99S00S01S02S03S04S05S06S07S08S09S10S11S12S13S14S15S16S17S19S20S21S22S23S24S25S26S27S28S29S30S31S32S33S34S35S36S37S38S39S40S41S42S43S44S45S46S47S48S49S50S51S52S53S54S55S56S57S58S59S60S61S62S63S64S65S66S67S68S69S70S71S72S73S74S75S76S77S78S79S80S81S82S83S84S85S86S87S88S89S90S91S92S93S94S95S96S97S98S99T07T14T15T16T17T18T19T20T21T22T23T24T25T26T27T28T30T31T32T33T34T36T37T38T39T40T41T42T43T44T45T46T47T48T49T50T51T52T53T54T55T56T57T58T59T60T61T62T63T64T65T66T67T68T69T70T71T73T74T75T76T78T79T80T81T82T83T84T85T86T87T88U07U09V00V01V02V03V04V05V06V09V10V11V12V13V14V15V16V17V18V19V20V21V22V23V24V25V26V27V28V29V30V31V32V33V34V35V36V37V38V39V40V41V42V43V44V45V46V47V48V49V50V51V52V53V54V55V56V57V58V59V60V61V62V63V64V65V66V67V68V69V70V71V72V73V74V75V76V77V78V79V80V81V82V83V84V85V86V87V88V89V90V91V92V93V94V95V96V97V98V99W00W01W03W04W05W06W07W08W09W10W11W12W13W1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Related Codes

Frequently Asked Questions

Is M34.1 a billable ICD-10-CM code?

Yes, M34.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

What does M34.1 mean?

M34.1 is the ICD-10-CM diagnosis code for "CR(E)ST syndrome". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of M34.1?

The parent code of M34.1 is M34 ("Systemic sclerosis [scleroderma]"). M34.1 provides a more specific classification within this category.

What section is M34.1 in?

M34.1 is located in Section M30-M36 — "Systemic connective tissue disorders" within Chapter 13 of the ICD-10-CM Tabular List.

What are the sub-codes of M34.1?

M34.1 has 1918 sub-code(s) that provide more specific detail: A00, A01, A02, A03, A04 and more.

When should I use M34.1?

Use M34.1 when the patients documented diagnosis matches "CR(E)ST syndrome" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for CR(E)ST syndrome?

The ICD-10-CM code for CR(E)ST syndrome is M34.1.

Can M34.1 be used for primary diagnosis?

Yes, M34.1 can be used as a primary diagnosis code since it is billable and specific.

What chapter is M34.1 in?

M34.1 is in Chapter 13 of the ICD-10-CM Tabular List.

Is M34.1 valid for 2026?

Yes, M34.1 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousM34.0Progressive systemic sclerosisNext →M34.2Systemic sclerosis induced by drug and chemical
Code Details
M34.1
CR(E)ST syndrome
Billable / Specific Code
13 — Diseases of the musculoskeletal system and connective tissue (M00-M99)
M30-M36 — Systemic connective tissue disorders
2026 ICD-10-CM