Q87.8
Non-Billable

Other specified congenital malformation syndromes, not elsewhere classified

Non-Billable / Non-Specific Code

What is Other specified congenital malformation syndromes, not elsewhere classified?

ICD-10-CM Q87.8 is the diagnosis code for Other specified congenital malformation syndromes, not elsewhere classified. This code falls under the section "Other congenital malformations" within Chapter 17 — Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0). It is a non-billable/non-specific ICD-10-CM code that should not be used for reimbursement. A more specific sub-code is required for billing. Medical coders and healthcare providers use this code to document and classify diagnoses in electronic health records, insurance claims, and clinical databases.

⛔ Excludes1

Coding Guidelines for Q87.8

⛔ Type 1 Excludes (Never code together)

The following conditions should never be coded at the same time as Q87.8. They are mutually exclusive:

  • Zellweger syndrome (E71.510)

ICD-10-CM Code Hierarchy

Understanding where Q87.8 sits in the ICD-10-CM classification helps ensure proper coding:

Current CodeQ87.8 — Other specified congenital malformation syndromes, not elsewhere classified
Sub-Codes (1918)
A00A01A02A03A04A05A06A07A08A09A15A17A18A19A20A21A22A23A24A25A26A27A28A30A31A32A33A34A35A36A37A38A39A40A41A42A43A44A46A48A49A50A51A52A53A54A55A56A57A58A59A60A63A64A65A66A67A68A69A70A71A74A75A77A78A79A80A81A82A83A84A85A86A87A88A89A90A91A92A93A94A95A96A98A99B00B01B02B03B04B05B06B07B08B09B10B15B16B17B18B19B20B25B26B27B30B33B34B35B36B37B38B39B40B41B42B43B44B45B46B47B48B49B50B51B52B53B54B55B56B57B58B59B60B64B65B66B67B68B69B70B71B72B73B74B75B76B77B78B79B80B81B82B83B85B86B87B88B89B90B91B92B94B95B96B97B99C00C01C02C03C04C05C06C07C08C09C10C11C12C13C14C15C16C17C18C19C20C21C22C23C24C25C26C30C31C32C33C34C37C38C39C40C41C43C44C45C46C47C48C49C4AC50C51C52C53C54C55C56C57C58C60C61C62C63C64C65C66C67C68C69C70C71C72C73C74C75C76C77C78C79C7AC7BC80C81C82C83C84C85C86C88C90C91C92C93C94C95C96D00D01D02D03D04D05D06D07D09D10D11D12D13D14D15D16D17D18D19D20D21D22D23D24D25D26D27D28D29D30D31D32D33D34D35D36D37D38D39D3AD40D41D42D43D44D45D46D47D48D49D50D51D52D53D55D56D57D58D59D60D61D62D63D64D65D66D67D68D69D70D71D72D73D74D75D76D77D78D80D81D82D83D84D86D89E00E01E02E03E04E05E06E07E08E09E10E11E13E15E16E20E21E22E23E24E25E26E27E28E29E30E31E32E34E35E36E40E41E42E43E44E45E46E50E51E52E53E54E55E56E58E59E60E61E63E64E65E66E67E68E70E71E72E73E74E75E76E77E78E79E80E83E84E85E86E87E88E89F01F02F03F04F05F06F07F09F10F11F12F13F14F15F16F17F18F19F20F21F22F23F24F25F28F29F30F31F32F33F34F39F40F41F42F43F44F45F48F50F51F52F53F54F55F59F60F63F64F65F66F68F69F70F71F72F73F78F79F80F81F82F84F88F89F90F91F93F94F95F98F99G00G01G02G03G04G05G06G07G08G09G10G11G12G13G14G20G21G23G24G25G26G30G31G32G35G36G37G40G43G44G45G46G47G50G51G52G53G54G55G56G57G58G59G60G61G62G63G64G65G70G71G72G73G80G81G82G83G89G90G91G92G93G94G95G96G97G98G99H00H01H02H04H05H10H11H15H16H17H18H20H21H22H25H26H27H28H30H31H32H33H34H35H36H40H42H43H44H46H47H49H50H51H52H53H54H55H57H59H60H61H62H65H66H67H68H69H70H71H72H73H74H75H80H81H82H83H90H91H92H93H94H95I00I01I02I05I06I07I08I09I10I11I12I13I15I16I1AI20I21I22I23I24I25I26I27I28I30I31I32I33I34I35I36I37I38I39I40I41I42I43I44I45I46I47I48I49I50I51I52I5AI60I61I62I63I65I66I67I68I69I70I71I72I73I74I75I76I77I78I79I80I81I82I83I85I86I87I88I89I95I96I97I99J00J01J02J03J04J05J06J09J10J11J12J13J14J15J16J17J18J20J21J22J30J31J32J33J34J35J36J37J38J39J40J41J42J43J44J45J47J4AJ60J61J62J63J64J65J66J67J68J69J70J80J81J82J84J85J86J90J91J92J93J94J95J96J98J99K00K01K02K03K04K05K06K08K09K11K12K13K14K20K21K22K23K25K26K27K28K29K30K31K35K36K37K38K40K41K42K43K44K45K46K50K51K52K55K56K57K58K59K60K61K62K63K64K65K66K67K68K70K71K72K73K74K75K76K77K80K81K82K83K85K86K87K90K91K92K94K95L00L01L02L03L04L05L08L10L11L12L13L14L20L21L22L23L24L25L26L27L28L29L30L40L41L42L43L44L45L49L50L51L52L53L54L55L56L57L58L59L60L62L63L64L65L66L67L68L70L71L72L73L74L75L76L80L81L82L83L84L85L86L87L88L89L90L91L92L93L94L95L97L98L99M00M01M02M04M05M06M07M08M10M11M12M13M14M15M16M17M18M19M1AM20M21M22M23M24M25M26M27M30M31M32M33M34M35M36M40M41M42M43M45M46M47M48M49M50M51M53M54M60M61M62M63M65M66M67M70M71M72M75M76M77M79M80M81M83M84M85M86M87M88M89M90M91M92M93M94M95M96M97M99N00N01N02N03N04N05N06N07N08N10N11N12N13N14N15N16N17N18N19N20N21N22N23N25N26N27N28N29N30N31N32N33N34N35N36N37N39N40N41N42N43N44N45N46N47N48N49N50N51N52N53N60N61N62N63N64N65N70N71N72N73N74N75N76N77N80N81N82N83N84N85N86N87N88N89N90N91N92N93N94N95N96N97N98N99O00O01O02O03O04O07O08O09O10O11O12O13O14O15O16O20O21O22O23O24O25O26O28O29O30O31O32O33O34O35O36O40O41O42O43O44O45O46O47O48O60O61O62O63O64O65O66O67O68O69O70O71O72O73O74O75O76O77O80O82O85O86O87O88O89O90O91O92O94O98O99O9AP00P01P02P03P04P05P07P08P09P10P11P12P13P14P15P19P22P23P24P25P26P27P28P29P35P36P37P38P39P50P51P52P53P54P55P56P57P58P59P60P61P70P71P72P74P76P77P78P80P81P83P84P90P91P92P93P94P95P96Q00Q01Q02Q03Q04Q05Q06Q07Q10Q11Q12Q13Q14Q15Q16Q17Q18Q20Q21Q22Q23Q24Q25Q26Q27Q28Q30Q31Q32Q33Q34Q35Q36Q37Q38Q39Q40Q41Q42Q43Q44Q45Q50Q51Q52Q53Q54Q55Q56Q60Q61Q62Q63Q64Q65Q66Q67Q68Q69Q70Q71Q72Q73Q74Q75Q76Q77Q78Q79Q80Q81Q82Q83Q84Q85Q86Q87Q89Q90Q91Q92Q93Q95Q96Q97Q98Q99QA0R00R01R03R04R05R06R07R09R10R11R12R13R14R15R16R17R18R19R20R21R22R23R25R26R27R29R30R31R32R33R34R35R36R37R39R40R41R42R43R44R45R46R47R48R49R50R51R52R53R54R55R56R57R58R59R60R61R62R63R64R65R68R69R70R71R73R74R75R76R77R78R79R80R81R82R83R84R85R86R87R88R89R90R91R92R93R94R97R99S00S01S02S03S04S05S06S07S08S09S10S11S12S13S14S15S16S17S19S20S21S22S23S24S25S26S27S28S29S30S31S32S33S34S35S36S37S38S39S40S41S42S43S44S45S46S47S48S49S50S51S52S53S54S55S56S57S58S59S60S61S62S63S64S65S66S67S68S69S70S71S72S73S74S75S76S77S78S79S80S81S82S83S84S85S86S87S88S89S90S91S92S93S94S95S96S97S98S99T07T14T15T16T17T18T19T20T21T22T23T24T25T26T27T28T30T31T32T33T34T36T37T38T39T40T41T42T43T44T45T46T47T48T49T50T51T52T53T54T55T56T57T58T59T60T61T62T63T64T65T66T67T68T69T70T71T73T74T75T76T78T79T80T81T82T83T84T85T86T87T88U07U09V00V01V02V03V04V05V06V09V10V11V12V13V14V15V16V17V18V19V20V21V22V23V24V25V26V27V28V29V30V31V32V33V34V35V36V37V38V39V40V41V42V43V44V45V46V47V48V49V50V51V52V53V54V55V56V57V58V59V60V61V62V63V64V65V66V67V68V69V70V71V72V73V74V75V76V77V78V79V80V81V82V83V84V85V86V87V88V89V90V91V92V93V94V95V96V97V98V99W00W01W03W04W05W06W07W08W09W10W11W12W13W14W15W16W17W18W19W20W21W22W23W24W25W26W27W28W29W30W31W32W33W34W35W36W37W38W39W40W42W44W45W46W49W50W51W52W53W54W55W56W57W58W59W60W61W62W64W65W67W69W73W74W85W86W88W89W90W92W93W94W99X00X01X02X03X04X05X06X08X10X11X12X13X14X15X16X17X18X19X30X31X32X34X35X36X37X38X39X50X52X58X71X72X73X74X75X76X77X78X79X80X81X82X83X92X93X94X95X96X97X98X99Y00Y01Y02Y03Y04Y07Y08Y09Y21Y22Y23Y24Y25Y26Y27Y28Y29Y30Y31Y32Y33Y35Y36Y37Y38Y62Y63Y64Y65Y66Y69Y70Y71Y72Y73Y74Y75Y76Y77Y78Y79Y80Y81Y82Y83Y84Y90Y92Y93Y95Y99Z00Z01Z02Z03Z04Z05Z08Z09Z11Z12Z13Z14Z15Z16Z17Z18Z19Z20Z21Z22Z23Z28Z29Z30Z31Z32Z33Z34Z36Z37Z38Z39Z3AZ40Z41Z42Z43Z44Z45Z46Z47Z48Z49Z51Z52Z53Z55Z56Z57Z58Z59Z60Z62Z63Z64Z65Z66Z67Z68Z69Z70Z71Z72Z73Z74Z75Z76Z77Z78Z79Z80Z81Z82Z83Z84Z85Z86Z87Z88Z89Z90Z91Z92Z93Z94Z95Z96Z97Z98Z99
Sub-Codes 9 entries
Q87.81Alport syndromeBillableQ87.82Arterial tortuosity syndromeBillableQ87.83Bardet-Biedl syndromeBillableQ87.84Laurence-Moon syndromeBillableQ87.85MED13L syndromeBillableQ87.86Kleefstra syndromeBillableQ87.87Hao-Fountain SyndromeBillableQ87.88CTNNB1 syndromeBillableQ87.89Other specified congenital malformation syndromes, not elsewhere classifiedBillable
Related Codes

Frequently Asked Questions

Is Q87.8 a billable ICD-10-CM code?

No, Q87.8 is a non-billable/non-specific code. You should use a more specific sub-code for billing and reimbursement.

What does Q87.8 mean?

Q87.8 is the ICD-10-CM diagnosis code for "Other specified congenital malformation syndromes, not elsewhere classified". It is used by healthcare providers to classify and document this condition in medical records and insurance claims.

What is the parent code of Q87.8?

The parent code of Q87.8 is Q87 ("Other specified congenital malformation syndromes affecting multiple systems"). Q87.8 provides a more specific classification within this category.

What section is Q87.8 in?

Q87.8 is located in Section Q80-Q89 — "Other congenital malformations" within Chapter 17 of the ICD-10-CM Tabular List.

What are the sub-codes of Q87.8?

Q87.8 has 1918 sub-code(s) that provide more specific detail: A00, A01, A02, A03, A04 and more.

When should I use Q87.8?

Use Q87.8 when the patients documented diagnosis matches "Other specified congenital malformation syndromes, not elsewhere classified" and the clinical documentation supports this level of specificity. Always verify with the latest ICD-10-CM guidelines and payer requirements.

People Also Ask

What is the ICD-10 code for Other specified congenital malformation syndromes, not elsewhere classified?

The ICD-10-CM code for Other specified congenital malformation syndromes, not elsewhere classified is Q87.8.

Can Q87.8 be used for primary diagnosis?

No, Q87.8 is non-billable. Use a more specific sub-code for primary diagnosis billing.

What chapter is Q87.8 in?

Q87.8 is in Chapter 17 of the ICD-10-CM Tabular List.

What conditions are excluded from Q87.8?

Type 1 Excludes for Q87.8 include: Zellweger syndrome (E71.510).

Is Q87.8 valid for 2026?

Yes, Q87.8 is a valid ICD-10-CM code for the 2026 fiscal year, subject to official CMS updates.

See Also

← PreviousQ87.5Other congenital malformation syndromes with other skeletal changesNext →Q87.81Alport syndrome
Code Details
Q87.8
Other specified congenital malformation syndromes, not elsewhere classified
Non-Billable / Non-Specific Code
17 — Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)
Q80-Q89 — Other congenital malformations
2026 ICD-10-CM